final exam-Table 1

Question 1

What are 2 important diagnostic tests for anemia?

Answer 1

Reticulocyte count, Hgb

Question 2

What does a high retic count with high bilirubin indicate?

Answer 2

Bone marrow is working!

Most likely d/t destruction or loss of RBCs (hemolytic)

Question 3

(acute/chronic) anemias are well tolerated in children

Answer 3

Chronic

Question 4

Anemic disorder characterized by bone marrow aplasia

Answer 4

Diamond Blackfan anemia

Question 5

Your patient presents with anemia + Petechiae. You suspect:

Answer 5

Leukemia or HUS

Question 6

Which lab would show you the presence of spherocytes?

Answer 6

Peripheral blood smear

Question 7

When does Fe deficiency anemia first appear?

Answer 7

After the first 4-5 mo of life

Question 8

What should you check if a pt presents with neutropenia or thrombocytopenia?

Answer 8

Bone marrow fxn

Question 9

Name the iron studies for Fe Deficient anemia

Answer 9

Serum ferritin (low)
Serum iron (low)
Total iron binding capacity (inc)
Transferrin saturation  (low)

Question 10

B-12 deficiency is a common finding in this GI disorder

Answer 10

Crohn’s

Question 11

Smooth beefy red tongue may indicate

Answer 11

B-12 deficiency

Question 12

Fanconi and Diamond-Blackfan anemias are ____ forms of normocytic anemia

Answer 12

Congenital

Question 13

____ can cause acquired normocytic anemia

Answer 13

Parvo B19

Question 14

What is TAR and what condition is it found in?

Answer 14

Thrombocytopenia with absent radius. Fanconi anemia

Question 15

Spherocytosis is inherited this way

Answer 15

Autosomal Dominant

Question 16

____ anemias are characterized by Anemia, Jaundice, Splenomegaly

Answer 16

Hemolytic

Question 17

Longstanding spherocytosis and sickle cell disease can cause _____

Answer 17

Gallstones

Question 18

What is the most common inherited enzyme defect?

Answer 18

G6PD deficiency

Question 19

G6PD commonly presents with this finding

Answer 19

Hyperbilirubinemia

Question 20

This hemoglobinopathy is found in carriers only

Answer 20

Thalassemia trait

Question 21

Thalassemia minor is a type of _____ thalassemia

Answer 21

Beta

Question 22

Hemophilias, vitamin K deficiency, and DIC are all disorders of _____

Answer 22

Coagulation

Question 23

Intrinsic clotting pathway is measured by a

Answer 23

PTT

Question 24

Extrinsic pathway measured with a

Answer 24

PT

Question 25

A pt who is bleeding into their joints should be worked up for

Answer 25

Hemophilia

Question 26

More common mechanism of thrombocytopenia

Answer 26

Increased consumption/ breakdown of RBCs

Question 27

____ is a type of thrombocytopenia associated with severe illness or shock

Answer 27

DIC

Question 28

Most common bleeding disorder of CHILDhood

Answer 28

ITP

Question 29

ITP usually shows up after____

Answer 29

A viral infection

Question 30

Treatment for ITP includes

Answer 30

``` Steroids IV Ig (in severe cases) ```

Question 31

Factor ___- and Von Willebrand work together

Answer 31

VIII

Question 32

_____ is the most common INHERITED bleeding disorder among Caucasians (though it can be acquired…)

Answer 32

Von Willebrand disease

Question 33

VW disease can be treated with _________, which releases vWF from endothelial stores

Answer 33

Desmopressin

Question 34

FFP contains____

Answer 34

All coag factors

Question 35

If you have abnormal PT/PTT, you would give

Answer 35

FFP

Question 36

If you have normal PT/PTT values, you would give

Answer 36

Cryoprecipitate

Question 37

Clotting problems are (more/less) common in kids than adults

Answer 37

Less

Question 38

First labs for a CA workup

Answer 38

CBC w/ diff | Peripheral blood smear

Question 39

ALL occurs most commonly in kids aged _____-______

Answer 39

2-10 (peak at 4)

Question 40

Most common CA treatment for kids

Answer 40

Chemo

Question 41

Philadelphia chromosome is associated with ____

Answer 41

CML | Chronic Myelogenous Leukemia

Question 42

Pt presents with firm, non-tender lymph node and hx cough. What do you order?

Answer 42

CBC CXR Lymph biopsy

Question 43

Hip dysplasia (is/is not) a disease of dislocation

Answer 43

Is NOT

Question 44

____ is the abnormal relationship between the proximal femur and acetabulum

Answer 44

Hip Dysplasia

Question 45

Hip dysplasia can be diagnosed using these techniques

Answer 45

Barlow’s and Ortolani’s maneuvers

Question 46

______ are indicative (not diagnostic) of hip dysplasia, occurring in up to 40% of cases

Answer 46

Asymmetric Skin folds

Question 47

Radial head subluxation is also known as

Answer 47

Nursemaid’s Elbow

Question 48

Typical posture associated with radial head subluxation

Answer 48

“my arm” posture

Question 49

Torus fractures are also known as

Answer 49

Buckle fracture

Question 50

Torus fractures affect these bones

Answer 50

Radius/ulnar

Question 51

___ is an oblique fracture of the distal tibia without a fibula fracture

Answer 51

Toddler’s Fracture

Question 52

Salter Harris classification describes ______ fractures

Answer 52

Epiphyseal

Question 53

A type _____ S-H fracture through a portion of the physis and epiphysis into the joint that may result in complication because of intra-articular component and because of disruption of the growing or hypertrophic zone of the physis.

Answer 53

Type III

Question 54

A type ____ S-H fracture presents as a crush injury to the physis with a poor functional prognosis

Answer 54

Type V

Question 55

This type of S-H fracture has joint involvement

Answer 55

Type III

Question 56

Most common bone tumor in children (benign)

Answer 56

Osteochondroma

Question 57

Most common malignant bone tumor in children

Answer 57

Osteosarcoma

Question 58

Anterior thigh and knee pain may be presentations of a ___ problem

Answer 58

Hip

Question 59

Joint pain can be an early presentation of ___-

Answer 59

Crohns Disease

Question 60

____ is the inflammation at the insertion of a ligament to a bone

Answer 60

Enthesitis

Question 61

You order an ANA on your patient. It comes back positive. What should be on your differential?

Answer 61

Lupus

Question 62

Most common site of pauciarticular arthritis

Answer 62

Knee

Question 63

___ often presents with a cyclic fever, salmon pink macular rash, and HSM

Answer 63

Systemic Form of JRA

Question 64

The 3 P’s of systemic JRA

Answer 64

Polyserositis Pleuritis Pericarditis

Question 65

First lab to order for suspected SLE

Answer 65

ANA

Question 66

Mainstay treatment for SLE

Answer 66

Steroids - methylprednisolone/ prednisone - hydroxychloroquin - NSAIDs

Question 67

Most common vasculitis in childhood

Answer 67

Henoch Schonelien Purpura

Question 68

Most likely cause of HA in kids

Answer 68

Migraine or tension HA

Question 69

Which of the following is NOT a test for MONO

Answer 69

CBC w/ diff Antibodies IGM Viral swab

Question 70

2yo w/ fever, dyspnea, sniffing dog position. | Swelling stops at midline

Answer 70

GROUP A STREP | retropharyngeal abscess

Question 71

RSV

Answer 71

Synagis is given as prophylaxis

Question 72

9 y/o Suspected URI, x-ray shows hyperinflation

Answer 72

Albuterol trial

Question 73

5 y/o amox w/ rash (erythema multiforme)

Answer 73

Oral antihistamines