Interstitial Lung Disease Flashcards
(9 cards)
Most common types of ILD
Idiopathic pulmonary fibrosis IPF
Connective tissue disease CTD
Hypersensitivity pneumonitis
What is interstitium
In between alveoli and vessels
Allows diffusion
Pathogenesis of IPF
Genetics
Premature aging of lungs
Worsened by smoking other risk factors
Injury to alveoli results in scaring and decreased function
Presentation of IPF
Lung crackles
How to ILD present on LFT
With a restrictive pattern due to fibrosis
ILD on CT
Honeycomb pattern is hallmark sign
Treatment for ILD
Steroids don’t work
Perfenidone and nintedanib slow the worsening and progression of disease
No cure
Lung transplant not available to most due to disease primarily affecting >75 Y/O and associated risks
Hypersensitivity pneumonitis
Caused by irritants like feather bedding, spores and mold
Treatment involves removing source of issue