Malrotation in a child Flashcards

1
Q

What is the definition of malrotation?

A

When the midgut doesn’t rotate fully around the superior mesenteric artery and the caecum ends up in the RUQ (instead of the RLQ)

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2
Q

What is the definition of volvulus?

A

A complication of malrotation

Complete twisting of an intestinal loop around the mesentery

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3
Q

What 2 broad things can happen in malrotation?

A

Small mesenteric base around which the bowel can rotate –> volvulus
Formation of Ladd bands from the peritoneum anterior to duodenum –> duodenal obstruction

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4
Q

What are the presenting features of malrotation?

A
Intermittent symptoms of obstruction
Bilious vomiting for the 1st few days of life
Non-bilious vomiting >2 months
Failure to thrive
Anorexia
Constipation
Recurrent abdo pain
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5
Q

In which patients is recurrent abdo pain more common in malrotation?

A

In older children

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6
Q

What are the presenting features of volvulus?

A
Rapid onset bilious vomiting -->
Metabolic acidosis
Lactic acidosis
Oliguria
Hypotension
Shock
Palpable abdo mass
Acute abdomen = distension and signs of peritonitis
Gangrene
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7
Q

What are the signs of gangrene in volvulus?

A

Tachycardia
Hypovolaemia
Septic shock

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8
Q

How is a diagnosis of malrotation or volvulus made?

A

Clinically

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9
Q

What is the role of investigations in malrotation?

A

Used for monitoring the severity of the disease

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10
Q

What lab investigations could be done in malrotation?

A

FBC - +WCC, +CRP

U+Es to detect dehydration, sepsis, and acidosis

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11
Q

What results from U+Es would suggest dehydration, sepsis, or acidosis in malrotation?

A

-Na+, +K+, met. acidosis, +urea, +creatinine, lactic acidosis

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12
Q

What signs of malrotation are seen on X-Ray?

A

Dilated small loops
Air-fluid levels
But may be normal

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13
Q

What signs of partial obstruction are seen on X-Ray?

A

Stomach and proximal duodenal dilation, distal bowel gas

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14
Q

What signs of complete duodenal obstruction are seen on X-Ray?

A

Gasless abdomen

Multiple dilated loops

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15
Q

What would contrast studies show in malrotation?

A

Misplaced duodenojejunal junction (at or to R of midline)

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16
Q

What would contrast studies show in volvulus?

A

Dilation of proximal duodenum and bird-beak obstruction + spiral duodenal configuration

17
Q

What is the mainstay of management of malrotation and volvulus?

A

Surgery - even in asymptomatic children

18
Q

What is the treatment of choice in malrotation and what is involved?

A

Ladd’s procedure
Involves untwisting the small bowel (anticlockwise), caecum, and appendix and put on the left, and the duodenum on the right

19
Q

What are complications of malrotation and volvulus?

A

Complete and persisting volvulus
Chronic intermittent volvulus
Short gut syndrome

20
Q

What is a possible consequence of complete/persisting volvulus?

A

Complete and persisting volvulus –> intestinal ischaemia, mucosal necrosis, and sepsis -(if untreated)-> perforation, peritonitis, death

21
Q

What is a possible consequence of chronic intermittent volvulus and how does it present?

A

Malabsorption

Constipation interspersed with diarrhoea

22
Q

What is short gut syndrome?

A

Malabsorption due to lack of functioning small bowel

23
Q

What does the prognosis of malrotation and volvulus depend on?

A

Degree of necrosis, especially after Ladd’s procedure

24
Q

What is mortality rate with midgut volvulus?

A

10%

25
Q

What is the chance of recurrence of voluvlus?

A

10%