Cognitive and Sensory Impairment Flashcards

1
Q

Cognitive impairment (CI) of intellectual disability is a general term that encompasses any type of mental difficulty or deficiency
Typ made when not meeting milestones - not reacting to environment in predictable way - not made at birth very often - seen when older unless know about genetic issue (Downs)
Diagnosis
Made after a period of suspicion by family or health professionals
In some instances, made at birth
Intellectual disability
Not interacting with environment in not predictable way or not interacting at all - not meeting milestones - can have large organ dysfunction

A

Cognitive impairment

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2
Q

Intellectual functioning
Subaverage intellectual function: IQ of 70 to 75 or below - normal 85-115
Functional strengths and weaknesses - something very good and big struggle for them
Younger than age 18 at the time of diagnoses

A

Intellectual disability

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3
Q

Genetic
Biochemical
Infectious - on meds while pregnancy; drugs or alcohol abuse; mom exposed to something (accutane - retinols on face) and same with adderoll
Familial - can be passed on
Social - more seen in severe abuse/neglect situations; no interactions
Environmental - more seen in severe abuse/neglect situations; no interactions
Organic

A

Cognitive impairment: etiology

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4
Q

Big goal: help them communicate; how can we talk to them - nonverbal things - sign language helpful - help fams adjust to this
Educate child and family
Early intervention
Teach child self-care skills
Promote child’s optimal development
Encourage play and exercise (socialization)
Provide means of communication
Establish discipline
Provide information on sexuality
Help families adjust to future care
Care for the child during hospitalization

A

Nursing care of children with impaired cognitive function

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5
Q

Most common neurodevelopmental disorder of childhood - very common
Lot less likely be diagnosed in females
Child with ADHD has a disruption in learning, socialization, and compliance (Leads to significant demands on parents, teachers, and the community.)
Specific diagnosis criteria
Pathophysiology
Symptoms usually appear by 7 years
Medications include:
Family support is very important
Educate parents
Understand goals of an IEP (Individualized education plan)

A

Attention deficit/Hyperactivity Disorder (ADHD)

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6
Q

Inattention/Distractibility
Impulsivity
Hyperactivity - constantly moving
Teachers - annoyed and overwhelmed - child does pick up on that - lot higher risk of anxiety; lot negative feedback from adults - negative self-talk
IEPs - treatment: meds

A

Most common neurodevelopmental disorder of childhood - very common

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7
Q

6 or more findings from specific category are present
Ex. Difficulty with attention, does not seem to listen, forgetful, losing thing easily, fidgeting, failing to remain sitting, talking excessively, interrupting often…

A

Specific diagnosis criteria

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8
Q

Not entirely understood but thought to be related to alteration in dopamine/norepinephrine neurotransmitters.
Strong Familial tendency

A

Pathophysiology

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9
Q

Psychostimulants
Methylphenidate (Ritalin)
Dexroamphetamine-Amphetamine (Adderall)
Nonstimulant norepinephrine reuptake inhibitors
Biggest concern: slow growing; not care to eat; take off during summer and not feel like self

A

Medications include:

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10
Q

Neurodevelopmental disorders
Etiology—Unknown - lots of theories; hereditary
Clinical manifestations and diagnostic evaluation
Care Management
Behaviors impact the child’s ability to communicate and interact with others
Diff areas can fall on spectrum
How help them if struggle it
Trouble with eye contact, not understand empathy; line up toys
Highlight things struggle with and help support them
Prematurity increases risk
Forgetfulness common
Implement things into daily life - checklists helpful; normal routine helpful as well
Common delays (at least 1)
Other expected findings:

A

Autism spectrum disorders (ASD)

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11
Q

Deficits in social interactions, communication, and behavior

A

Clinical manifestations and diagnostic evaluation

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12
Q

Interprofessional care
Family support

A

Care Management

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13
Q

Social interactions
Social communication
Imaginative play

A

Common delays (at least 1)

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14
Q

Distress when routines are changed
Unusual attachments to objects
Inability to start or continue conversations
Grunting or humming
Delayed or absent language development
Lack of empathy

A

Other expected findings:

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15
Q

Can be a severely disabling condition
No cure for autism
Some improvement with language skills
Numerous therapies used
Autism often becomes a family disease
Frequently parents express guilt and shame - commonly feel that fams fault; some science and blame self
Stress importance of family counseling
Autism Society of America is good source of information
Clients should be managed at home or in long-term placement facility

A

ASDs: care management

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16
Q

Recognize early
Often have motor dysfunction - do things diff - motor funcs not work normally
Attempt behavior modification
Provide a structured routine
Decrease unacceptable behavior

A

Numerous therapies used

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17
Q

Prevalence (In the US)
Identified through vision screening programs
Etiology
Types
Trauma
Infections

A

Visual impairment

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18
Q

Prenatal or postnatal infections
Retinopathy of prematurity
Trauma
Postnatal infections
Other disorders
Sickle cell disease
Juvenile rheumatoid arthritis
Tay-Sachs disease
DM

A

Etiology

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19
Q

Refraction
Bending of light rays through the lens of the eye
Myopia (bigger issue because of screens and tablets) - number one cause detached retina, Hyperopia, Amblyopia
Strabismus (may or may not be refractive)

A

Types

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20
Q

Want to prevent this
Protective eyewear
Common cause of blindness in children
Penetrating:
Nonpenetrating
Treatment: Aimed at preventing further damage

A

Trauma

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21
Q

Conjunctivitis
Not treated properly can lead to blindness - can do eye drops if done early enough - not as common
Ophthalmic antibiotics
Systemic antibiotics in some cases

A

Infections

22
Q

Nursing assessment
Nursing alert
Promote parent-child attachment
Promote child’s optimal development
Education
Provide a safe environment
Hospitalized Child

A

Caring for the visually impaired child

23
Q

Not react to changes in light
Pupils never change
Harder screen younger kids
Identify children who by virtue of their history are at risk
Observe for behaviors that indicate a vision loss
Screen all children for visual acuity
Snellen letter, tumbling E, or picture chart - talk

A

Nursing assessment

24
Q

Suspect visual impairment in a child of any age whose pupils do not react to light - assess as much visual
Know have - support child and fam - bond as well as can - promote optimal development; want have independence; hospital - provide reassurance; orient to room - not change locations of things

A

Nursing alert

25
Q

Independence
Play and socialization

A

Promote child’s optimal development

26
Q

Braille
Audio books and learning materials

A

Education

27
Q

Provide reassurance during all treatments
Orient child to surroundings
Encourage independence
Treatment team members should be consistent

A

Hospitalized Child

28
Q

More common
Esp if child in NICU
Hearing at adult level when born - premature - sensitive to loud noises; NICU - quiet and loud noises down
Worry about kidneys and speech - understanding
Etiology:
Conductive (middle ear) - benefit from hearing aids; type have some delay - small batteries and love put in mouth - sleeping - take out
Sensorineural (inner ear/nerve damage) - benefit from cochlear implants; type have some delay - small batteries and love put in mouth - sleeping - take out
Parents as teachers - recognizing things like hearing loss early so not fall behind - quicker caught up - better for child
Mixed conductive-sensorineural
Central auditory imperceptions (functional hearing loss)

A

Hearing impairment

29
Q

Family Hx
Anatomic malformations
Perinatal asphyxia
Infections
Substance abuse
Chronic ear infections - most common reason
Cerebral Palsy
Downs sydrone
ELGAN - prematurity
Ototoxic drugs (genatmycin), O2 requirments

A

Etiology:

30
Q

Aphasia - hear and understand - cannot form words
Agnosia - talking to and cannot understand what saying

A

Central auditory imperceptions (functional hearing loss)

31
Q

Lack of startle reflex
Absence of reaction to auditory stimuli
Absence of well-formed syllables by age 11 months
General indifference to sound
Lack of response to spoken word

A

Infancy - Manifestations

32
Q

Kids not talking
Loud monotone voice if not diagnosed - rare get to point
Profound deafness: Likely to be diagnosed in infancy
If not detected in infancy, identified upon entry into school
Abnormalities in speech development
Learning disabilities

A

Childhood - Manifestations

33
Q

Lipreading
Cued speech
Sign language
Speech language therapy
Additional aids
Socialization
Support child and family
Reassess understanding of instructions given
Supplement with visual and tactile media
Provide communication devices
Picture board with common words
Assistance of child life specialist
Additional aids

A

Care management

34
Q

Common
Downs most common
Often have:
Increased risk of autosomal trisomy’s seen with AMA (advanced maternal age) - older mom is more likely for mom to have this
Examples: Tay-Sachs, Prader-Willi, Angelman, Cri-du-chat, Wolf-Hirschhorn, Beckwith-Wiedemann - thousands

A

Chromosomal abnormalities

35
Q

Intellectual disabilities
Learning disabilities
Behavioral problems
Distinct features (including birth defects)

A

Often have:

36
Q

Most common chromosome abnormality
Causes unknown; probably multiple
Occurs in populations of all races
Nonfamilial trisomy 21
Increases with increased maternal age
Clinical manifestations
Chromosome analysis
High risk
Physical problems
Available therapies
Prognosis
Care management

A

Down syndrome

37
Q

Square head with upward slant to eyes - eyes widespread and low - low set ears - sign chromosomal abnormality
Flat nasal bridge - nose under developed, protruding tongue
Hypotonia - floppy - lot longer to meet milestones

A

Clinical manifestations

38
Q

Strabismus
Herscrupung’s
Leukemia
CHD - septal defects
DDHD

A

High risk

39
Q

Congenital heart disease
Hypothyroidism
Leukemia
Hip subluxation
Decreased muscle tone
Hirschsprung’s disease
Tracheoesophageal fistula
Strabismus/nystagmus

A

Physical problems

40
Q

What child presenting and struggling with
Surgery to correct congenital anomalies
Evaluation of hearing and sight
Periodic testing of thyroid function

A

Available therapies

41
Q

Expectancy white: 40 yrs
Expectancy black: 20 yrs - more likely more severe heart defects
Other ethnicities: 10 yrs
Part disparities in healthcare

A

Prognosis

42
Q

Supporting child’s family at time of diagnosis
Preventing of physical problems
Assist in prenatal diagnosis and genetic counseling

A

Care management

43
Q

Second most common genetic cause of cognitive impairment after Down syndrome
Caused by abnormal gene on the lower end of the long arm of the X chromosome - deals with abnormal gene
Large head circumference and large face
In males and females; males more symptomatic and males severe; females more carries and some manifestations
Can reproduce
Long face with a prominent jaw (prognathism)
Large, protruding ears
Large testes (postpubertal)
Manifestations variable in female carriers of gene
Classic Behavioral Features
Therapeutic Management

A

Fragile X syndrome

44
Q

Mild-to-severe cognitive impairment
Delayed speech and language - confused for ADHD; some ASD behaviors; treatment sim to those
Hyperactivity
Hypersensitivity to taste, sounds, and touch
Autistic-like behaviors
Aggressive behaviors

A

Classic Behavioral Features

45
Q

Tegretol/Prozac for behavioral control
Stimulants for hyperactivity (similar to management of attention deficit/hyperactivity disorder)
Referral to early intervention program
Prognosis
Normal life span expected
Care management
Genetic counseling - passed on to siblings

A

Therapeutic Management

46
Q

Sex chromosome abnormality
May only have one X
Only females present with this
Usually diagnosed in early childhood
Cannot reproduce
No cure
Hormonal therapy typically initiated - give estrogen
Therapeutic management focuses on managing the health issues related to the syndrome.

A

Turner syndrome

47
Q

Short stature
Failure to grow
Failure to growth
More likely have osteoporosis, overweight, heart issues, cognitive impairment, no estrogen

A

Usually diagnosed in early childhood

48
Q

In males
Present with feminine features, Cognitive delays
Missed early age - assume has ADHD - struggle in school; learning disabilities; unless do genetics
Small testes; gynecomastia, fat deposits not typ see in male pop
Around puberty realize something more going on
Most common sex chromosomal abnormality
One or more X chromosome is present
Often times not diagnosed until adolescence or adulthood
Males present with female-like physical features (testosterone deficiency)
No cure
Infertility may be of concern - majority time are infertile
Therapeutic management focuses on managing the health issues related to the syndrome.

A

Klinefelter Syndrome

49
Q

Lack of secondary sex characteristics
Cognitive impairments such as motor delay, speech delay, attention deficits, and learning disabilities

A

Often times not diagnosed until adolescence or adulthood

50
Q

Hormonal therapy typically initiated - given testosterone
Very tall typ
Cosmetic surgery

A

Therapeutic management focuses on managing the health issues related to the syndrome.