ebstein's anomaly

Question 1

what is ebstein’s anomaly

Answer 1

congenital heart defect characterised by low insertion of the tricuspid valve resulting in large atrium and small ventricle

Question 2

what in utero drug might ebstein’s anomaly be related to

Answer 2

lithium

Question 3

associations with ebstein’s anomaly

Answer 3

patent foramen ovale or atrial septal defect
wolff-parkinson-white

Question 4

clinical features of ebstein’s anomaly

Answer 4

cyanosis
prominent a wave in JVP
hepatomegaly
tricuspid regurgitation: pansystolic murmur
RBBB

Question 5

management of ebstein’s anomaly

Answer 5

echo to confirm
medical management: treat arrhythmias and HF
surgical: tricuspid valve repair