Immunodeficiency Flashcards

1
Q

Primary B cell

A

X linked agammaglobulinaemia- early sev bact infec
Hyper IgM synd- bact infec and PCP
IgG subclass defic- recurr resp infec

Test Ig levs and func vacc resp

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
2
Q

primary T

A

SCID- first few mnth, fail thrive, persis viral and fungal infec

FBC, film, lymphoc subsets and func

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
3
Q

primary neut

A

Leucocyte adhesion defic- inflant delayed healing, ulcers, bact, fung

Chemotaxis, adhesion molecs, killing

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
4
Q

secondary

A
CA
Imm supp drugs
HIV
Splenectomy
Nephrotic synd
SCD
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
5
Q

Multisys synd

A

DiGeorge

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
6
Q

mx

A
Proph abx
Supp care and abx for infecs
Repl Ig and addit vacc
Bm transpl
Gene therapy future
How well did you know this?
1
Not at all
2
3
4
5
Perfectly