Nephrology

Question 1

Benign Familial Hematuria

Answer 1

Thin Basement Membrane Nephropathy

Question 2

Management of Edema in Minimal Change Disease

Answer 2

salt restriction

Question 3

Most Common Cause of Hydronephrosis in infancy

Answer 3

Ureteropelvic junction obstruction

Question 4

Coca Colored Urine + Viral Illness

Answer 4

IgA Nephropathy

Question 5

Calcium Oxalate crystals, think

Answer 5

ethylene glycol ingestion (antifreeze)

Question 6

What is deposited in anti-GBM disease

Answer 6

IgG and C3

Question 7

What age to repair a hydrocele

Answer 7

1 year of age

Question 8

ARPKD Features

Answer 8

Potter facies
palpable kidneys
hepatic fibrosis

Question 9

Treatment of urethral prolapse

Answer 9

estrogen cream

Question 10

PIGN Complement Levels

Answer 10

Low C3

normal C4

Question 11

Inguinal Hernias should be repaired…

Answer 11

at diagnosis

Question 12

Urethrorrhagia

Answer 12

hematuria at the ending of urinating in boys

Question 13

When to being screening of proteinuria in DM

Answer 13

T1DM 3-5 years

T2DM at time of diagnosis

Question 14

Hypoplasia or abscence of patella
Dystrophic Nails
Renal Disease

Answer 14

Nail-Patella Syndrome

AD

Question 15

Most Common Thrombosis Sites in Nephrotic Syndrome

Answer 15

Sagittal Sinus

Renal Vein

Question 16

Aminoglycoside - mechanism of renal toxicity

Answer 16

ATN

Question 17

RTA That Causes Renal Stones

Answer 17

Type 1 - Distal

Question 18

Salt Losing Nephropathy w/o signs of nephritis or nephropathy

Answer 18

Juvenile Nephronophthisis

Question 19

Prune Belly Syndrome

Answer 19

Cryptoorchidism
Abscence of Abd Wall Musculature
Dilation of bladder/urethra/etc

Question 20

penile foreskin cannot be retracted =

Answer 20

phimosis

Question 21

Most Common Cause of Bilateral Urinary Obstructions

Answer 21

Posterior Urethral Valves

Question 22

Toxocara canis

Answer 22

dog roundworm

Question 23

Most Specific Test for Acute EBV

Answer 23

Viral Capsid Antigen (VCA) IgM

Question 24

Prune Belly Associated with ?hydroamions

Answer 24

oligohydroaminos –> pulmonary hypoplasia

Question 25

Elevated BP - 2017 Guidelines

Answer 25

BP > 95%tile | 13 years: >120/80

Question 26

When to further evaluate hypospadias

Answer 26

undescended testes or ambiguous genitlaia

Question 27

silk glove sign

Answer 27

think inguinal hernia

Question 28

Liddle Syndrome

Answer 28

primary Na retention | HTN, hypokalemia

Question 29

Bartters & Gitelman Syndromes

Answer 29

Barters - Loop, hypercalciuria, normal Mag | Gitelman - HCTZ, low Mag

Question 30

RTA Type 1

Answer 30

distal defect, impaired H+ secretion | elevated pH

Question 31

Causes of Type 1 RTA

Answer 31

Amp B, SLE, Sjogren

Question 32

RTA Type 2

Answer 32

proximal defection, decreased bicarb resoprtion | acidic pH

Question 33

Causes of Type 2 RTA

Answer 33

Fanconi Syndrome, Cystinosis

Question 34

Causes of Type 4 RTA

Answer 34

obstructive nephropathy

Question 35

Denys-Drash Syndrome

Answer 35

infant-onset nephrotic syndrome, renal failure by 3 years

Question 36

Symptoms of Medullary Sponge Kidney

Answer 36

Frequent UTIs, hematuria, renal stones

Question 37

Bardet-Beidel Syndrome

Answer 37

obesity, cystic dysplasia of kindey, retinitis pigmentosa

Question 38

Liddle & Gordon Syndrome

Answer 38

HTN Liddle: pseudoaldosteronism Gordon: pseudohypoaldosteronism