Paediatrics Flashcards

1
Q

HIGH FEVER, SORE THROAT, SOFT INSPIRATORY STRIDOR AND DROOLING

A

acute epiglottitis - infection of epiglottis caused by Haemophilus influenzae
- it causes oedema of the epiglottis
- causes obstruction of airways and difficulty breathing
- drooling caused by patients not swallowing their saliva due to throat being really sore
- LEAN FORWARDS TO BREATHE

EMERGENCY

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2
Q

CROUP PRESENTATION

A
  • cough and common cold symptoms
  • inspiratory stridor
  • EMERGENCY

caused by parainfluenza virus
barking like cough
hoarseness

dexamethasone

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3
Q

MEASLES PRESENTATION

A

cough, cold like symptoms (cough, sneezing etc) conjunctivitis and white spots in the mouth and maculopapular rash

starts behind the ear then spreads to the rest of the body

INFECTED TILL AFTER 4 DAYS OF INFECTION

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4
Q

TEST FOR MEASLES

A

IgM antibodies from blood or saliva

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5
Q

BABY BORN AT TERM, VAGINAL DELIVERY BUT THERE IS A SWELLING ON BABY’S HEAD

CROSSES SUTURE LINES, BABY IS WELL

A

this is Caput Succedaneum: collection of fluid in the head due to pressure on the head during a vaginal delivery

resolves in a few days

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6
Q

LONG HISTORY OF COUGH, WHEEZE, STINKY AND GREASY LOOSE STOOLS, NASAL POLYPS AND POOR GROWTH

A
  • most likely to be cystic fibrosis
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7
Q

CHILDREN WITH CYSTIC FIBROSIS ARE DEFICIENT OF WHICH VITAMINS

A

A, D, E AND K

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8
Q

NEONATAL JAUNDICE RISK FACTORS

A

PREMATURE BIRTH
BREASTFEEDING

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9
Q

LETHARGY, HEADACHE, SORE THROAT, RUNNY NOSE AND FEVER
RED RASH ON TORSO AND CHEEKS THAT BLANCHES UNDER PRESSRE

A

SLAPPED CHEEK SYNDROME
supportive management

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10
Q

WHICH BILLIRUBIN IS RAISED IN PHYSIOLOGICAL NEONATAL JAUNDICE

A

UNCONJUGATED

  • more rbcs in babies so more turnover so more billirubin is made to be broken down
  • immature liver in babies is not able to break down the unconjugated billirubin into cojugated so babies have more unconjugated billirubin in their blood
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11
Q

SLAPPED CHEEK SYNDROME NAME

A

Erythema infectiosum

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12
Q

FEVER, CHEST PAIN IN THE LAST 24 HOURS IN CHEST AND BACK, AND SHORTNESS OF BREATH AND SICKLE CELL DISEASE

A

ACUTE CHEST SYNDROME

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13
Q

ACUTE ONSET OF CHEST PAIN THAT IS WORSE ON DEEP INSPIRATION AND MOVEMENT

what is it?

A

CONSTROCHONDRITIS

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14
Q

ACUTE BREATHLESSNESS AND PLEURITIC CHEST PAIN BUT NORMAL BREATH SOUNDS - NO CRACKLES OR WHEEZING

A

PULMONARY EMBOLISM

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15
Q

POOLING OF BLOOD WITHIN ORGANS THAT CAUSE WORSENING ANAEMIA
ABDOMINAL PAIN AND PALPABLE MASS IN LEFT UPPER QUADRANT

A

SEQUESTRATION CRISIS

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16
Q

BONE MARROW IS NO LONGER ABLE TO MAKE ENOUGH NEW RED BLOOD CELLS.
SYMPTOMS OF FEVER, MALAISE, PALLOR, SOB, PALPITATIONS

A

APLASTIC CRISIS

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17
Q

TEST FOR DEVELOPMENTAL HIP DYSPLASIA

A

Barlow and ortolani tests

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18
Q

RISK FACTORS FOR DEVELOPMENTAL HIP DYSPLASIA

A

FEMALE, FIRST BORN AND CHILD AND BREECH PRESENTATION

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19
Q

WHAT DOES THE BARLOW AND ORTOLANI TEST INVOLVE?

A

BARLOW - attempt to dislocate the femoral head
ORTOLANI - attempt to relocate the femoral head

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20
Q

VESICULAR RASH ON PALMS, SOLES AND BUCCAL MUCOSA WITH FEVER
what is it and what causes it?

A

Hand-foot mouth disease
caused by: Coxsackie A virus

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21
Q

COXSACKIE B VIRUS CAUSES WHAT

A

myocarditis

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22
Q

TACHYPNOEA AND DISTRESS SHORTLY AFTER BIRTH AND HYPERINFLANTION OF LUNGS AND FLUID IN HORIZONTAL FISSURE

A

TRANSIENT TACHYPNOEA OF NEW BORN (TTN)

  • generally resolves after first day and needs oxgen therapy
  • caused due to delayed reabsorption of fluid in the lungs
  • associated with c-sectionq
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23
Q

DEFICIENCY OF SURFACTANT IN PREMATURE NEONATES: RESPIRATORY DISRESS, TACHYPNOEA, GRUNTING AND CYANOSIS.
BECOMES MORE SEVERE AFTER BIRTH

A

NEONATAL RESPIRATORY DISTRESS SYDROME
- chest x ray shows glass lungs and bell shaped thorax

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24
Q

morbiliform reaction - what is it

A

common in patients with mononucleosis taking amoxicilin

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25
circular rashes that are blister like that happen every time drug is taken
fixed drug reaction
26
rosea rash
rash followed after upper RTI
27
what are urticarial rash
hives
28
joint pain and fever joint pain for over 6 weeks and pink rash in young child what is it
juvenile idiopathic arthritis
29
what is juvenile idiopathic arthritis a complication of?
anterior uveitis
30
what does immune thrombocytopenic purport cause
rash all over the body
31
henlock Schonlein Purpura symptoms
purpuric rash over buttocks and extensor surfaces
32
projectile vomiting after feeds
pyloric stenosis test for this with ultrasound
33
perianal itching that is worse at night
thread worm treat with mebendazole
34
coxsackie virus a16 what does it cause
fever, rash around mouth and ulcers on hands and feet
35
patient presents with sore throat and fever has raised white cells and low platelets and blast cells presentation: bruising, enalarged lymph nodes and fatigue what is the most likely diagnosis
acute lymphocytic leukaemia - very common in children
36
potter syndrome
pressure in utero due to oligohydramnios
37
small baby non-productive cough not feeding well high RR high HR low BP and low O2 what is the diagnosis
bronchiolitis due to RSV virus
38
when should babies pass meconium by?
24 hours after birth concerning if not
39
what happens when baby does not pass meconium within 24 hours?
no stool swelling in the abdo bilious vomiting - this means obstruction in the bowels
40
what is hirschspungs disease
within the GI tract the ganglionic layer in the intestinal walls which develops in the neural crest helps with the detection of stool in this disease - there is a lack of the ganglionic cells so this part of the bowel doesn't work so stool cannot be passed
41
symptoms of hirschspungs disease
no meconium passed from baby in over 24 hours swelling in the abdo bilious vomiting
42
management of hirschspungs disease
surgical management
43
investigation for hirschspungs disease
investigation is done based on the part where the obstruction is biopsy
44
where is the obstruction if stool comes out after doing rectal examination in hirschspungs disease?
there is a lack of ganglions in the rectum
45
why are antibiotics given to children before any procedure if they have ventricular septal defects?
to prevent the risk of them developing infective endocarditis
46
what is the prophylactic medication given for RSV virus
Palivizumab (Any monoclonal antibodies) prevents children against bronchitis
47
what are the symptoms of RSV
very common in young children runny nose difficulty breathing crepitations cough child is off feeds
48
autism presents as what in children?
social distancing playing by themselves not talking in full sentences not making eye contact
49
cerebral palsy presents in children as?
stiffness motor developmental delay
50
what is the more specific test for bacterial sepsis
procalcitonin
51
chicken pox produces what type of rashes?
maculopapular vesicular rashes which are very itchy all over the face and body
52
presentation of measles
blanching maculopapular rash all over the body grey spots in the mouth
53
complications of measles found in developing countries
vitamin A deficiency
54
common complications of measles
Subacute sclerosing panencephalitis - affects brain and degenerates it causes loss of cognition and seizures can affect person up to 10 years of measles infection
55
what is broncholitis obliterans
it is a condition which causes inflammation of the bronchioles the airways become scarred which then causes them to narrow
56
what is the most common cause behind broncholitis obliterans
adenovirus
57
what is primary nocturnal enuresis
bed wetting as a child
58
what is given to children with nocturnal enuresis
prescribe desmopressin if child is over 7 if not then given enuresis alarm - this detects if there is water in the bed and alarm sets off - reminds child to go to the toilet
59
what is given if child has nocturnal enuresis and increased frequency of urination
oxybutynin
60
what is physiological jaundice
occurs in neonates because their livers are not fully developed so unable to convert unconjugated bilirubin to conjugated bilirubin - this builds up in the blood and causes jaundice
61
management of physiological jaundice
it goes away in 7-10 days found within 24 hours of birth when baby is slightly jaundiced at birth but levels of bilirubin are in the normal range
62
what is pathological jaundice
jaundice caused by a particular external cause eg. haemolysis due to RH factor or O factor this can cause a toxic buildup of unconjugated bilirubin
63
what are the complications of pathological jaundice
this can spread through the blood brain barrier and damage the brain causes athetoid cerebral palsy in the long run
64
what is turners syndrome
XO karyotype condition affects women late menopause small breasts wide spaced nipples
65
what is slipped upper femoral epiphysis
weakness in the femoral growth plate happens due to obesity and common in males common cause of limping in adolescents
66
perthe's disease - what is it
blood supply to the femoral head is blocked so the head of femur begins to die weakened bone begins to break apart from the joint when blood supply is restored - the hip joint heals - but in the duration when it didn't receive blood, if it loses shape then it can cause stiffness and pain
67
what is meconium ileus
over 48 hour delay in passing stool after birth and has features of bowel obstruction like bilious vomiting
68
what is seen on x-ray if baby has meconium ileus
'bubbly' appearance
69
what is Noonan syndrome
genetic condition that stops normal development in different parts of the body developmental delays short stature heart defects
70
trisomy 18 is what condition
Edwards syndrome
71
XXY karyotype causes what condition?
Klinfelter's syndrome
72
trisomy 13 causes what condtion
Patau syndrome
73
bronchiolitis vs bronchiolitis obliterans
broncholitis gets better by itself broncholitis causes permanent narrowing of the airways
74
symptoms of broncholitis obliterans
dry cough breathlessness SOB fever wheeze harsh breath sounds crepitations
75
symptoms of perthes disease
limping pain in the joint difficulty rotating the leg pain that is worse on movement better on rest
76
typical presentation of slipped upper femoral epiphysis
knee pain
77
symptoms of Noonan syndrome
eyes - down slanting and droopy eyelids ears - rotated backwards face - appears droopy and expressionless head - larger and low hairline
78
heart conditions caused due to Noonan syndrome
valve disorders - pulmonary valve stenosis hypertrophic cardiomyopathy ventricular septal defect irregular heart rhythm
79
MSK symptoms of Noonan syndrome
wide set nipples spine deformity sunken sternum short webbed neck
80
what is Edwards syndrome
affects growth in baby happens when person has extra copy of chromosome 18 development defects
81
symptoms of Edwards syndrome
low set ears reduced muscle tone overlapping fingers eg. finger clubbing small head congenital heart diseases renal failure bowel wall defects
82
what is Klinefelter syndrome
boys are born with extra copy of X chromosome affects testicules lower testosterone reduced facial hair enlarged breast tissue reduced fertility
83
signs and symptoms of Klinefelter syndrome
muscle weakness delay in speaking testicles haven't descended to the scrotum taller than normal long legs, broad hips small penis difficulty in speaking/reading
84
what is Patau syndrome
physical disabilities heart diseases brain/spine abdnormalities small, poorly developed eyes extra fingers/toes
85
what is the foramen ovale
it is the opening between the left and right atrium allows blood to flow from the left to the right atrium
86
fetal circulation cycle
- oxygenated blood from the placenta goes through the umbilical vein into the IVC - it enters the right atrium - it goes from the right atrium to the left atrium via the foramen ovale and into the aorta to the rest of the body - the lungs are fluid filled so their resistance is high which stops blood circulation to the lungs - deoxygenated blood goes to the internal iliac arteries and then umbilical artery and back to the placenta to get oxygenated
87
how does the foramen ovale close
when the baby takes the first breath - the lungs expand - this causes decrease in resistence - pressure in the right atrium then decreases - pressure in the left atrium increases this causes the foramen ovale to close
88
what is ventricular septal defect
most common congenital heart disease - when there is a hole between the left and right ventricles - the pressure is higher in the left than right so this is the way the blood flows
89
what is a small/medium/large ventricular septal defect
small - no consequences as only small amount of blood moves past the hole medium - blood from left side will enter right and enter pulmonary circulation this makes the left side of the heart bigger large - blood goes from the left to right, causes pulmonary hypertension so then pressure on right side increases, blood moves back to left side called - Eisenmengers syndrome
90
symptoms of eisenmengers syndrome
cyanosis and clubbing in the fingers restrictive - loud pan systolic murmur non-restrictive - pulmonary hypertension and heart failure and murmur is softer
91
what is an atrial septal defect
hole in the septum that separates the two - blood flows from left atrium to right - right side gets bigger - causes breathlessness - pulmonary pressure increases due to increased blood flow to right side - causes murmur due to increased flow across the pulmonary valve
92
what is patent ductus arteriosus
the ductus arteriosus doesn't close after birth - happens to babies who are premature and maternal rubella indomethacin - prostaglandin inhibitor is given - stimulates closure of the duct
93
grades of patent ductus arteriosus
silent - very small and no murmur small - there is a murmur but no effects moderate - loud murmur, displaced apex beat large - murmur is silent as pressures have equalised
94
coarctation of the aorta
narrowing of the aorta symptoms: hypertension headaches nosebleeds cold legs examination - weak and delayed pulse in the legs BP in right arm is higher than left arm
95
why cannot live injections be given to children on chemotherapy
because the children will be immunosuppressed and so injecting a live vaccine in them will cause them to get severely ill
96
what is a Hickman line
the central line put inside for children who need their bloods taken, give drugs or chemo always important to check this Hickman line as it can get infected
97
what are the common side effects of chemo therapy
anaemia neutropenia - high risk of getting an infection that can develop into sepsis - so if a child comes in with fever and neutropenia then treat quickly
98
what is given to children with neutropenia
G-CSF to increase WBC count
99
what is the longterm ladder management for asthma
1. preventers - corticosteroids and ICS like becthamethasone 2. leukotine inhibitors - monterlukast 3. LABA like salmetrol - has to be prescribed by specialists
100
what is reactive arthritis
arthritis that presents post infection
101
what is perthes disease
when there is a loss in the blood supply to the hip joint - this causes some parts of the bone to get ischaemic and die - this can change the shape of the bone a little bit - this will mean that when the blood circulation is restored, the bone will not fit perfectly in the joint as it has changed shape - this will cause difficulty and pain when moving common in children (boys) aged 5-6 years
102
what is transient tenosynovitis
it is the most common cause of hip pain in children under 10 more common in right hip than left can be due to trauma or infection - may be post respiratory tract infection - pain will be on the anterior aspect of the thigh - inflammation of the synovial joint
103
what is osteomyelitis
infection of the bone - can be due to bacterial infection symptoms: - fever - swelling - warmth and redness of the area - fatigue common in smokers
104
why are most neonates jaundiced when they are born
-physiological jaundice - goes away after 2 weeks - liver is too small to convert unconjugated bilirubin to conjugated bilirubin - unconjugated bilirubin builds up - bilirubin is the product of the death of haemoglobin - too high levels are toxic - can cause brain damage in neonates
105
when to know if the jaundice in neonates is pathological and not physiological
test is done - if the level of bilirubin is higher than a threshold then it is suspected for pathological jaundice
106
what is pathological jaundice
when the high levels of bilirubin cannot be dealt by the liver high levels of unconjugated bilirubin stays in the blood - this happens due to higher levels of haemolysis - so higher number or RBCs are broken down
107
what are the two types of unconjugated hyperbilirubinea
immune and non immune immune - eg. RH factor group incompatibility or ABO group causes haemolytic of the babies blood - raises levels of unconjugated bilirubin
108
when are conjugated bilirubin levels raised?
when there is an issue with the liver eg. Gamma-glutamyl Transferase is an enzyme in the liver that converts unconjugated bilirubin to conjugated - this enzyme is defected in Gillberts syndrome and Angler Wajjar syndrome - - this causes raised levels of conjugated bilirubin in the blood
109
what's biliary atresia
congenital disease - blockage in the bile ducts - bile cannot flow from the liver into the bowel to be excreted - so conjugated bilirubin accumulates in the liver - do surgery to prolong life - should be done in the first 8 weeks of life
110
what is breast milk jaundice
found in babies that are exclusively breast fed there is an inhibitor in the milk that inhibits action of the Gamma-glutamyl Transferase - causes raised unconjugated bilirubin levels
111
what type of jaundice does cystic fibrosis cause
can cause unconjugated and conjugated jaundice - mucus can build up and block the bile ducts - but very likely to be picked up on in early age - children will also have weight Loss, fatigue and failure to thrive
112
what is therapy is used in jaundice
phototherapy -
113
what are the symptoms of SLE in children
butterfly rash on the face other systemic issues malar rash swelling pain in joints
114
symptoms of juvenile idiopathic arthritis
rheumatoid arthritis that happens in children salmon-pink rash on the legs and knees
115
symptoms of chrondomalacia patellae
swelling of the patella but no systemic symptoms
116
osgood disease - what is it
similar to perthes but doesn't cause weight loss or fever
117
Henoch-Schönlein Purpura
inflammatory disease of the small blood vessels starts off with symptoms of: fever, rash on legs, abdo pain - then red or purple spots start to appear on the skin
118
what is whooping cough
it is a bacterial infection caused by pertussis it is the bacteria that is given a vaccine for in the DPT vaccine - causes cough then inspiratory gasp - runny nose - fever and cyanosis use macrolide antibiotic - clarithromycin doesn't treat the infection - it reduces the chances of child passing it onto someone else
119
what is transposition of the great arteries
when the pulmonary artery and aorta are switched in places deoxy blood from the body come to heart but then gets repumped back to the body oxygenated blood comes from the lungs but goes back to the lungs procedure done to correct this - atrial switch procedure complication of the correction is - tricuspid regurgitation
120
what is Reyes syndrome
aspirin shouldn't be given to children younger than 12 years causes acute liver failure raised bilirubin INR is prolonged raised lactate raised creatinine
121
What is diphtheria
- highly infectious - affects nose and throat - rare in UK - part of the DPT vaccine symptoms: - fever - sore throat - swollen cervical lymphs - difficulty breathing - thick grey-white coating that covers back of throat can also cause blisters and ulcers on the legs, feet and hands
122
what is tetanus
survives for a long time outside the body found in the soil or poo of animals part of the DPT vaccine for children can get infected by: cuts on skin, burns etc symptoms: stiffness of jaw muscles muscle spasms fever sweating tachycardia
123
what is Pertussis
part of the DPT vaccine - whooping cough chest infection - common in babies symptoms: runny nose sore throat between coughs children gasp for air redness of face can become cyanosed
124
polio in children
- given to children 3 times at 12 weeks old, 3yrs4months and 14 years booster spreads from contaminated poo symptoms - fever - tiredness - headaches - vomiting - muscle pain - in serious cases can cause paralysis
125
Haemophilus influenzae type b (Hib)
it can cause meningitis septicaemia pneumonia spread via nose and throat of healthy people
126
hepatitis B - vaccine given to children
infection of the liver spread via bloods and bodily fluids symptoms: loss of appetite being sick diarrhoea abdo pain jaundice
127
MMR Vaccine
measles - cold like symptoms and red eyes, white spots in mouth, watery eyes, measles rash, Mumps - causes swelling in the parotid gland, can cause swelling of testis and ovaries, deafness, fever, headache etc Rubella - German measles - causes red/pink rash, swollen lymph nodes, fever, aching joints rash - pink/red coloured itchy starts behind the ears then spreads to the head and neck
128
what is a moro reflex?
a startled reflex baby's response to a loud noise they will tilt their head back and stretch out their legs and arms and maybe start to cry - goes away after 3-6 months
129
rickets - what is it and what does it cause
it is vitamin D deficiency - caused due to reduced sun exposure in children - esp those who have coloured skin children who are breast fed for a long time are also at risk as breast milk is not a good source of vitamin D symptoms of this - bowed legs, wrist and ankle swelling, muscle weakness and delayed walking
130
scurvy - what is it and symptoms
causes bone pain and easy bruising vitamin c deficiency
131
foetal alcohol syndrome
cause behind developmental delay children will have developmental delay will have delayed motor skills poor coordination difficulty in language and social skills
132
what is discoid eczema
eczema that has circular lesions
133
transient tachypnoea of the newborn
happens 2 hours after delivery goes away after 72 hours child will be breathless and have low O2 sats
134
what is tuberous sclerosis
genetic condition that causes benign tumours to develop in different parts of the body can cause developmental delays seizures behavioural problems
135
what is third nerve palsy
when the eye looks down and out at rest
136
what is fourth nerve palsy
the eye cannot look down and inwards towards the midline superior clique muscle is paralysed patient may present with eye looking up and in at rest head may be tilted to compensate for this
137
what is sixth nerve palsy
lateral rectus muscle is paralysed eye cannot look away from the nose (abduct horizontally)
138
orbital cellulitis features
extreme case of pre septal cellulitis painful eye movements swollen eye lid erythema
139
pre septal cellulitis features
swollen eye lid erythema mild fever 1. visual impairment 2. diplopia - double vision 3. painful eye movements
140
retinitis pigmentosa
cause behind retinal degeneration causes history of night blindness and reduced visual fields
141
what drops are used for acute angle closure glaucoma
pilocarpine - reduces intraocular pressure which causes closure of the eye ball
142
nephroblastoma - what is it
Wilm's tumour embryonic tumour that is found in the kidneys most common abdo mass in children causes symptoms of - haematuria - hypertension -fever - abdo mass
143
the pertussis virus can cause?
whooping cough
144
grunting is a sign of?
respiratory distress in babies
145
neonatal respiratory distress syndrome
common in premature babies - due to not enough pneumocystis - so not enough surfactant is produced - there is not enough surfactant in the plural space - this increases surface tension - so the alveoli cannot expand properly - can cause the lungs to collapse - give artificial surfactant
146
coxsackie virus causes what disease?
hand, foot and mouth disease
147
what is juvenile idipathic arthritis
rheumatoid arthritis in young children - gradual onset - morning stiffness no systemic symptoms pain in the joints
148
symptoms of patent ductus arteriosis
baby will have a collapsing pulse machine like murmur bradycardia episodes of when they stop breathing
149
what medication can be given to help in patent ductus arteriosis
indomethacin - it causes vasoconstriction which causes the duct to close
150
what is intestinal malrotation
is when during the foetal development, the mid gut rotates and blocks off the blood supply - this causes a 'corkscrew' appearance on the Xray - it also is a big cause behind bilious green vominting - it is managed by a surgical procedure (Ladd bands)
151
jejunal atresia
causes bilious vomiting in newborn babies abdominal distension but on X ray - looks like a 'triple bubble'
152
duodenal atresia
bilious vomiting in babies abdo distension X ray appearance - 'double bubble'
153
meconium ileus
when the large intestine is blocked due to the meconium being really thick - can be due to mucus this causes a 'bubbly' looking Xray
154
most common congenital heart defect in neonates with diabetic mothers?
transposition of the great arteries
155
diagnostic test for CF
sweat test - 2 electrodes on skin which causes sweating, the sweat is analysed for sodium chloride which is high in CF the transmembrane protein transports sodium chloride, and water if there is dysfunction in this then sodium chloride levels increase children with CF 'taste salty' it causes respiratory and pancreatic secretions to become thick so this causes obstruction
156
what is meckels diverticulum
most common congenital abnormality of the intestine it is a bulging left over of the umbilical cord the vitelline duct does not close properly in the 5th week of feral development leaving this pouch behind - common presentation is GI bleeding
157
antibodies for coeliac disease
anti TTG antibodies small bowel biopsy for young children
158
Kawasaki disease - what is it
affects coronary arteries it can cause aneurysm development do echocardiogram
159
nocturnal enuresis - what factors affect It
bladder capacity ability to wake up and use toilet amount of urine that is being produced
160
pathology behind nocturnal enuresis
ASH increases at night so more water is retained which is why urine is dark in the morning and concentrated this is nocturnal ADH secretion this is not fully developed in children which is why desmopressin is given as a treatment for children who are bed wetting
161
factors that increase incontinence chances
bladder capacity - it is reduced in children but improves with age caffeine irritates the bladder UTI - Inflammation of the bladder so it is more irritated
162
what is given in overactive bladder
urge incontinence oxybutynin
163
coarctation of the aorta
it is a congenital narrowing of the aorta it causes a systolic murmur heard at the scapula and also radio-femoral delay babies with turners syndrome also have coarctation of the aorta
164
Vesicouretric reflux - what is it
when the urine travels back up the ureters due the valves not working properly this can cause recurrent UTIS - needs surgery
165
presentation of GORD in babies
recurrent vomiting chronic cough and slow growth this is due to the oesophageal spincter growing slowly in premature babies which can cause reflux
166
when should babies start walking
18months
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what is intussusception
it is when a part of the bowel collapses in itself making a telescope like shape it causes jelly stools and a sausage mass in the abdomen abdo discomfort baby is in a lot of pain and holds legs up do lapratomy
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what is benign Rolandic epilepsy
it is a type of epilepsy that is common in children 3-13 years - they generally outgrow it after puberty - have seizures in the night - CENTOTEMPORAL SPIKES ON EEG
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what is benign Rolandic epilepsy
it is a type of epilepsy that is common in children 3-13 years - they generally outgrow it after puberty - have seizures in the night - CENTOTEMPORAL SPIKES ON EEG
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eye condition in premature babies due to prematurity
prematurity that requires the administer of foetal oxygen is a risk for premature retinopathy due to abnormal and uncontrolled development of blood vessels in the eye
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What sort of symptoms does a ventricular septal defect
Ventricular septal defect a lot left lower standard edge, harsh pansystolic murmur. Will be Heard which will cover the whole systole and will extend from the first and second hearts down and children present with failure to thrive - if left untreated - can cause pul. hypertension as shunting will start happening r-l eisenmengers syndrome
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What symptoms are seen in mitral stenosis
Mid diastolic murmer I would generally be a history of rheumatic fever in the child
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What are the features of a patent ductus arteriosus?
It will present with a machine like Mama, which is continuous at the left upper sternal edge This is due to a left right shunting of blood so more blood is going to the lungs increased risk of respiratory tract infections and also left sided. Hypertrophy children would present with failure to thrive.
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What are the features of aortic septal defect?
It is a acyanotic, congenital heart condition Blood will be chanting from left to right or starts with normal. More blood will be going to the right side which would create an ejection systolic murmur in the pulmonary area. Generally will not be heard in the beginning but as the symptoms get worse, you can start to hear it. In this condition, more oxygenated blood is entering back into the Pulmonary system and deoxygenated blood and up, going back through the body
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What are the acyanotic congenital heart defect?
Ventricle septal defect, patent, ductus arteriosus, and atrial septal defect
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What are the cyanotic congenital heart defect?
Transposition of the great arteries and tetralogy of fallout
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What is tetralogy of fallot characterised by
ventricular septal defect, overriding aorta, pulmonary stenosis and right ventricular hypertrophy.
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What are the features in transposition of the great arteries
In this condition, the right artery and right ventricle are connected to the aorta and the left artery and a ventricle and connect to the pulmonary artery. So in this case, the right side which has deoxygenated blood pumps blood through the aorta into the systemic circulation oxygenated blood which comes from the left side of the heart, is connected to the pulmonary artery and goes into the pulmonary circulation In this case, the baby will be very cyanotic as no oxygen will be reaching the body In this case, the only way the baby can survive is, if they had a ASD VSD or a PDA. This will allow the mixing of oxygenated blood into the systemic circulation. If this is not there, then the baby can die.
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What is the immediate management used for transposition of the great arteries
Step one is to give prostaglandin that will allow the doctors arteriosus to remain open and this will allow the mixing of the blood In any normal situation, the doctors arteriosus stays open for 24 to 48 hours after birth and then closes, but giving prostaglandin will allow this to remain open The doctors arteriosus closes due to the drop in prostaglandin after birth Step two is to do an atrial septostomy, so make a hole in the heart to allow the mixing of blood then the switching operation is done
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What are the features of tetralogy of fallot
There is pulmonary stenosis in which the pulmonary artery is more narrow. This obstruction means that less blood enters the pulmonary circulation. This makes the right side bigger because it has to work harder. - due to the right ventricular hypertrophy, there is increase pressure on the side of the heart. This causes the shunting to be from right to left This is the VSD, and due to the overriding aorta it means that deoxygenated blood passes the lungs and goes from the right ventricle into the left ventricle, and then into the water, and then into the systemic circulation. So deoxygenated blood gets passed around the body.
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What are some of the symptoms of tetralogy of fallot seen in children?
Children present with cyanotic spells in which the left ventricle goes into spasm. loud murmur heard on upper sternal edge hypoxic and cyanotic baby goes blue The way to manage this is giving morphine to reduce the heart rate and blood pressure Phenylephiline - This increases systemic pressure and causes the shunt to reverse and go from right to left to left -> right
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management of impetigo
topicsl hydrogen peroxide cream fusicidic acid send to school after 48 hours off starting sntibiotics or after crusting over
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lice symptoms
itchy neck and rash pediculuous capitis mgt - wet combing insecticide dimethicone gel - can be used in pregnant mathalion aqueous liquid
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how to refain from school in chicken pox
until lesions have crusted over
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chicken pox appearance
starts with fever then rash starts at the head then spreads over the body
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causative organism of measles
parxmyovirus
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most common complication of measles
otitis media, pneumonia and encephalitis
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feature of mumps
swelling on the face and can also sometimes get epiorchitis - swelling of the testes supportable management complication is pancreatitis
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features of rubella
also known as German measles rash that spares the limbs togavirus headache low grade fever spotty and red all over rash - forcheimer spots on the soft pallet of the mouth
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complications of rubella
serious risk to pregnant women - in first 20 weeks can cause cataracts, ductus arteriosus and Brian damage can't give mmr vaccine to pregnant women
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molluscum contagiosa features
small dome shaped pupils with a central umbilication pearly coloured itchy painless contagious - generally clears after a few months
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roseola infantam features
really high fever after fever suddenly the rash appaers maculopapapular rash blanching starts on the trunk and spreads outwards human herpes virus 6 supportive management
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slapped check syndrome features
parvovirus fever diarrhoea slapped cheeks can cause aplastic crisis - aneamia in children contagious until rash appears
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scarlet fever features
strep progenes swollen tonsils sandpaper rash strawberry tongue - white coating on the red tongue sore throat headache and fever
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management of scarlet fever
throat swab oral penicillin for 10 days can return to school 24 hours after antiobtics have been started
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Wilms nephroblastoma
buzz words ' painless palpable lump in the RUQ of abdo' common in children under 5 refer in 48 hours spreads quickly new lump in the abdo
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what is the most common kidney cancer in children
wilms tumour - very common in children under 5
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investigation of intussecpition
- ultrasound
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intussecpition features
the colon folds in on it self severe abdo pain sausage shaped mass in RUQ pain red current stool children draw up legs targets seen in the ultrasound
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management of intussuception
air enema - pass air through the bowel most common cause of bowel obstruction in children
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necrotising enterocolitis features
- premature infants - necrosis of the bowel gas within the bowel wall intolerance to feeds x-ray shows: dilated bowel loops and within the bowel wall air in the bowel and biliary tree
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what is hirchsprungs disease
delaying in passing of the meconium (24hours) chronic constipation the end section of the bowel is not innervated so there is delay in passing of meconium - baby passes poo after sticking finger up the anus - associated with Down syndrome
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management of hirchsprungs disease
renal biopsy is gold standard rectal washouts, or do surgery
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volvulus sign on x ray
coffee bean sign
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abdominal migraine
abdo pain lasting an hour but everything else is normal
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mesenteric adenitis features
can mimic appendicitis - rebound tenderness and very painful no fever or other systemic upset follows recent viral infection enlarged mesenteric lymph nodes but normal appendix
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appendicitis in children features
pain very very painful nausea and vomiting fever will be there very rigid abdo
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jaundice presentation before 24 hours
always pathological G6PD deficiency haemolytic anaemia
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jaundice presentation after 24 hours
often normal - physiological jaundice due to the liver common in breast fed babies
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jaundice presentation after 14 days
do further investigation : hypothyroidism biliary atresia UTI congenital infections or autoimmune haemolytic anaemia
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Gilberts sydrome
presentation of jaundice in older children (teens) generally during stressful times
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pyloric stenosis features
ABG - metabolic alkalosis projectile vomiting poor feeding failure to thrive olive shaped mass in the epigastric region poor weight gain
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pyloric stenosis investigation
ultrasound of abdo
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management of pyloric stenosis
laparoscopic pyloromyotomy
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GORD in babies features
vomiting after larger feeds milky due to over feeding after being laid flat crying while feeding
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side effects of PPIS in babies
high sodium in gaviscon can cause vomiting and constipation
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nocturnal enuresis - management
1. enuresis alarm and reduced fluid intake before bed 2. desmopressin (short term control)