peds uworld

Question 1

girl with primary amenorrhea with no sense of smell

Answer 1

kallman syndrome

Question 2

are FSH and LH elevated or depressed in Turners?

Answer 2

elevated

Question 3

which rash manifests as hypopigmented lesions with surrounding darker area and itchy

Answer 3

tinea versicolor

Question 4

which rash is christmas tree distribution on trunk?

Answer 4

pityriasis rosea

Question 5

CBC results for sickle cell splenic sequestration

Answer 5

anemia
increased reticulocytes
dec platelets

Question 6

reye syndrome on liver biopsy shows

Answer 6

microvesicular steatosis

Question 7

ppx for household contacts for pertussis

Answer 7

macrolide abx- regardless of age, sxs, vaccine status

Question 8

sturge weber syndrome presentation

Answer 8

Port wine stain on face
leptomeningeal cap-venous malformation
ID
seizures
visual field defects

Question 9

legg calves perthes disease on x ray

Answer 9

avascular necrosis- flattened fragmented femoral head

Question 10

treatment for common variable immunodeficiency

Answer 10

IVIG

Question 11

treatment for prolonged QTc syn

Answer 11

beta blockers, pacemaker

prevent with nl lytes and avoid meds that induce it

Question 12

whats gold standard dx for duchennes?

Answer 12

genetic testing of dystrophin gene

Question 13

can kids skip to treatent for strep throat if fulfill all centor criteria?

Answer 13

no, must be tested. only adults can skip

Question 14

centor criteria

Answer 14

fever
tender LAD
tonsillar exudates
no cough

Question 15

treatment for strep throat

Answer 15

penicillin or amoxicillin

Question 16

are flaky peeling hands and feet normal in newborn?

Answer 16

yes

Question 17

what are pink stains in diaper newborns represent?

Answer 17

uric acid crystals- nl first week

Question 18

does testicular cancer risk go down with cyptochordism who’s undergone orchiopexy?

Answer 18

yes, but still higher than general pop

Question 19

both bruton agammaglobuminemia and CVID have decreased Igs all around, but which one has also low B cell count?

Answer 19

bruton agammaglob

decrease total lymphocytes - CD4 to get B cell #

Question 20

what is this ear dz? chronic ear drainage for weeks, new onset hearing loss, skin debris and granulation tissue

Answer 20

cholesteatoma - congenital or acquired (2/2 middle ear dz)

Question 21

breath holding spells

Answer 21

benign brief apnea and color change

emotional trigger

6 mo- 2yrs

Question 22

clavicle fracture treatment

Answer 22

self- resolve within 10 days- gently handle

Question 23

which is most common cause of pneumonia in CF patient under 20 and over 20

Answer 23

under 20: staph aureus

over 20: pseudomonas

Question 24

Lesch Nyhan syndrome

Answer 24

x-linked defect in HGPT pathway

ID, dystonia, chorea, spasticity

self-mutilation

gouty arthritis

Question 25

asymmetric resp distress, think...

Answer 25

foreign body aspiration

Question 26

dx and tx of foreign body aspiration

Answer 26

bronchoscopy

Question 27

milk or soy protein induced colitis

Answer 27

2-8 weeks vomiting, bloody diarrhea, eczema switch to hydrolyzed formula

Question 28

herpangina (coxsackie A) vs herpetic gingivostomatitis locations of oral lesions

Answer 28

cox: posterior oropharynx HSV: anterior oropharynx and lips

Question 29

is PaO2 nl in methemoglobunemia?

Answer 29

yes but pulse ox is low (decreased oxygen delivery to tissues, but still bound to Hgb)

Question 30

antidote to methemoglobunemia?

Answer 30

methylene blue

Question 31

antidote to lead poisoning

Answer 31

dimercaprol

Question 32

antidote to ethylene glycol or methanol

Answer 32

fomipizole

Question 33

marfanoid body habitus sxs

Answer 33

``` pectus deformity tall: lower>upper, long arms skin hyperplastic joints lax scoliosis ```

Question 34

homocystinuria vs marfan syndrome distinguishing features

Answer 34

both have marfanoid body habitus marfan: normal intellect, aortic root dilation, upward lens dislocation homo: ID, thrombosis, downward lens dislocation

Question 35

homocystinuria is a defect in

Answer 35

cystathione synthase

Question 36

homocystinuria treatment

Answer 36

B6, B12, folate anticoagulation or antiplatelet to prevent stroke

Question 37

serum sickness-like reaction

Answer 37

hypersensitivity III 1-2 weeks after beta lactams or bactrum (or hep B, immune complex dz) fever, rash, polyarthlagia

Question 38

cephalohematoma vs caput succedanum

Answer 38

ceph: subperiosteum, doesnt cross suture lines, resorbs caput: superficial, crosses suture lines

Question 39

patient with hx of cyanotic congenital heart dz and recurrent sinusitis would lead to what which causes what triad?

Answer 39

brain abscess fever, FND, HA

Question 40

most common bacteria to cause otitis externa (swimmers ear)

Answer 40

pseudomonas

Question 41

do abscence seizures have post ictal period?

Answer 41

no

Question 42

1st step to evaluate primary amenorrhea

Answer 42

pelvic US- uterus present?

Question 43

do patients without mullerian duct have nl FSH and LH?

Answer 43

yes, because ovaries unaffected

Question 44

goals of SpO2 in newborn at minutes 0, 1-5, 5-10

Answer 44

0: 60% 1-5: 80% 5-10: 90% if under, do pos pressure ventilation

Question 45

do CPR on baby if HR under

Answer 45

60