further issues on CF

Question 1

what are 2 important issues with cystic fibrosis?

Answer 1

fertility issues

transplantation issues

Question 2

does CF havve an effect of sexual function?

Answer 2

no

Question 3

what gender does CF mostly affect with fertility?

Answer 3

men

Question 4

what are the options for male that are infertile?

Answer 4

Adoption
Artificial insemination with donor sperm (AID) 60-70% success rate

Intra-cytoplasmic sperm injection (ICSI)

Question 5

what nuber for FEV1 shows they are bad enough to have a lung transplant?

Answer 5

<30% predicted

Question 6

what factors would show a patient is bad enough to have a lung transplant?

Answer 6

FEV1 <30% predicted
Weight loss ++
Hypoxia at rest/de-saturation on exercise
Hypercapnia
Recurrent worsening sepsis
Worsening quality of life

Question 7

what three questions should you ask before allowing patient to have lung transplant?

Answer 7

Is the condition bad enough?

Is the rest of the body good enough?

Does the patient want this (prepared to take a gamble …)

Question 8

what are the contra-indications to transplant ?

Answer 8

Other organ failure

Malignancy within 5 years

Significant peripheral vascular disease

Drug, nicotine, alcohol dependency

Active systemic infection

Microbiological issues (eg. M. abscessus)

Question 9

what are psychological issues regarding transplantation?

Answer 9

Hope

Fear

Guilt/conflict

Stress