Cystic Fibrosis Test 2

Question 1

How do you obtain cystic fibrosis?

Answer 1

autosomal recessive genetic disorder

Question 2

How do you diagnose CF?

Answer 2

sweat test of 60 or more indicated a positive reading of CF

• 39 indicates it’s negative
• 40-59 needs further testing

Question 3

What parts of the body are affected with CF?

Answer 3

Respiratory, GI, and reproductive

Question 4

How does CF affect the Respiratory system?

Answer 4

thickened mucous obstructs the airway

Question 5

How does CF affect the GI?

Answer 5

Thickened secretions obstruct bile and decrease motility

• Meconeum ileus: baby poop gets stuck in the intestines (causes: abdominal distention, steatorrhea (fatty stool), rectal prolapse, jaundice, and liver cirrhosis
• pancreas: enzyme damage (cannot absorb vitamin ADEK); causes inadequate insulin leading to failure to thrive and DM

Question 6

How does CF affect reproduction?

Answer 6

low sperm count=infertility

Question 7

What is the proper diet for CF patients?

Answer 7

high sodium, high protein high-fat diet

• take pancreatin before all meals to aid in digestion
• -may mix it in with acidic food like applesauce and NOT ALKALINE (dairy) because it will make enzyme not work