erythrpocyte Flashcards

(49 cards)

1
Q

aerobically converts glucose to pentose and produces NADPH

A

hexose mnophosphate shunt

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2
Q

most common enzyme deficiency in the pentose phosphate pathway

A

G6PD DEFICIENCY

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3
Q

RECOMMENDED SCREENING TEST FOR G6PD DEFICIENCY

A

G6PD FLUORESCENT SPOT TEST

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4
Q

A SCREENING TEST FOR 6G6D DEFICIENCY WHERE THE PATTERN IS SLIGHTLY TO MODERATE INCREASED BUT IS PARTIALLY CORRECTED BY GLUCOSE

A

AUTOHEMOLYSIS

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5
Q

CLAASIFICATION OF G6PD SEVERELY DEFICIENT
CLINICAL MANIFESTATION: HNSHA
VARIANTS: G6PD - SERRES AND G6PD MADRID

A

CLASS 1

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6
Q

CLAASIFICATION OF G6PD SEVERELY DEFICIENT
CLINICAL MANIFESTATION ASSOCIATED WITH FAVA BEANS AND FAVISM AND AY REQUIRED TRANSFUSION DURING HEMOLYTIC EPISODES
VARIANTS G6PD: MEDITERRANEAN
G6PD: CHATAM

A

CLASS 2

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7
Q

CLAASIFICATION OF G6PD MODERATELY TO MILDLY DEFICIENT
CLINICAL MANIFESTATION: SELF LIMITED, EPISODIC
VARIANTS:G6PD A AND G6PD CANTON

A

CLASS 3

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8
Q

CLAASIFICATION OF G6PD MILDLY DEFICIENT
CLINICAL MANIFESTATION NONE
VARIANTS: G6PD B AND G6PD A THAT MAY ALSO MANIFEST CLASS 3

A

CLASS 4

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9
Q

CLAASIFICATION OF G6PD INCREASED ACTIVITY
CLINICAL MANIFESTATION NONE
VARIANTS NONE

A

CLASS 5

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10
Q

MAINTAINS IRON IN THE HEME IN ITS REDUCED STATE

A

METHEMOGLOBIN REDUCTASE PATHWAY

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11
Q

FOR THE PRODUCTION OF 2,3- BPG

A

RAPOPORT-LEIEBERING SHUNT

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12
Q

THE CURVE WHEN THE 2 VARIABLES ( PARTIAL PRESSURE OF OXYGEN AND AFFINIY OF HB0 ARE PLOTTED ON TEH GRAPH

A

OXYGEN DISSOCIATION CURVE

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13
Q

A SHIFT IN TEH CURVE DUE TO ALTERATION IN PH
EFFECT OF HYDROGEN INS AND CO2 ON TEH AFFINITY OF HEMOGLOBIN FOR OXYGEN

A

BOHR EFFECT

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14
Q

DEPICTS THE OCCURRENCE BY WHICH THE BINDING OF O2 TO THE HB PROMOTES THE RELEASE OF CO2

A

HALDANE EFFECT

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15
Q

SHIFT TO THE LEFT OR SHIFT TO THE RIGHT
INCREASED PH
DECREASED PCO2
DECREASED 2,3-BPG
DECREASED TEMPERATURE

A

SHIFT TO THE LEFT

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16
Q

V SHIFT TO THE LEFT OR SHIFT TO THE RIGHT
INCREASED PH
DECREASED PCO2
DECREASED 2,3-BPG
DECREASED TEMPERATURE
WHAT IS THE AFFINITU?

A

INCREASED

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17
Q

SHIFT TO THE LEFT OR SHIFT TO THE RIGHT
DECREASED PH
INCREASED PCO2
INCREASED 2,3-BPG
INCREASED TEMPERATURE

A

SHIFT TO THE RIGHT

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18
Q

SHIFT TO THE LEFT OR SHIFT TO THE RIGHT
DECREASED PH
INCREASED PCO2
INCREASED 2,3-BPG
INCREASED TEMPERATURE
WHAT IS THE AFFINITY

A

DECREASED

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19
Q

INCREASED NUMBER OF RED CELLS WITH VARIATION IN SIZE

A

ANISOCYTOSIS

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20
Q

LARGER THAN NORMAL RBC.
USUALLY SEEN WHEN NCV IS GREATER THAN 100
ASSOCIATED WITH IMPAIRED DNA

21
Q

SMALLER THAN NORMAL
USUALLY SEEN WHEN THE MCV IS <80 FL
ASSOCIATED WITH DEFECTIVE HEMOGLOBIN FORMATION

22
Q

BLOOD CELL HISTOGRAM THE X AXIS IS FOR:

23
Q

BLOOD CELL HISTOGRAM THE Y AXIS IS FOR

A

NUMBER OF CELLS

24
Q

TWO PARAMETERS CALCULATED FRIM RBC HISTOGRAM

25
IF THE RBC ARE MICROCYTES TE CURVE WILL SHIFT TO
RIGHT
26
IF THE RBCS ARE MACROCYTIC THE CURVE WILL SHIFT. TO THE
LEFT
27
IF THE HISTOGRAM CURVE IS BIMDAL THEN THERE ARE
TWO POPULATION OF RBC IN THE SAMPLE
28
WHAT CAN CAUSE BIMODAL DISTRIBUTION
BLOOD TRANSFUSION COLD AGGLUTINATION HEMOLYTIC ANEMIA WITH SCHISTOCYTE PRESENT
29
A CALCULATED INDEX GIVEN BY HEMATOLOGY ANALYZERS TO HELP IDENTIFY ANISOCYTOSIS AND PROVIDE INFORMATION ABOUT ITS DEGREE
RED CELL DISTRIBUTION WIDTH
30
BASED IN BITH THE WIDTH OF THHE RBC DISTRIBUTION CURVE AND THE MEAN RBC SIZE DEPENDENT BY WIDTH AND MCV
RDW-CV
31
THE ACTUAL MEASUREMENT OF THE WIDTH OF THE RBC DISTRIBUTION CURVE IN FL NOT INCLUENCED BY MCV
RDW SD
32
BETTER AND MOST RELIABLE MEASURE OF RBC VARIABILITY SPECIFICALLY IN HIGH ABNORMAL CONDITIONS
RDW-SD
33
WHEN WILL BE THE RDW DECREASE IN NEWBORNS
6 MOS OF AGE
34
VARIATION IN THE NORMAL COLOR
ANISOCHROMIA
35
OCCURRENCE OF HYPOCHROMIC CELLS AND NORMOCHROMIC CELLS IN THE BLOOD SMEAR
ANISOCHROMIA
36
ANISOCHROMIA CAN BE SEEN IN
SIDEROBALSTIC ANEMIA HYPOCHROMIA AFTER TRANSFUSION WITH NORMAL CELLS WEEKS AFTER IRON THERAPY FOR IDA
37
GRADING OF HYPOCHROMIA
1+ AREA OF CENTRAL PALLOR = 1/2 DIAMETER 2+ AREA OF CENTRAL PALLOR = 2/3 3+ AREA OF CENTRAL PALLOR = 3/4 4+ AREA OF CENTRAL PALLOR = THIN RIM OF HB
38
BC WITH A THIN RIM OF HEMOGLOBIN AND A LARGE CLEAR CENTER
ANULOCYTE/ PESSARY CELL OR GHOST CELL
39
ANULOCYTE MGHT BE SEEN IN
IRON DEFICIENCY ANEMAI
40
BASICALLY THE ONLY DISEASE IN WHICH THE MCHC IS HIGH
HHEREDITARY SPHEROCYTOSIS
41
HS HAS 3 KEY CLINCIAL MANIFESTATION
SPLEENOMEGALY ANEMIA JAUNDICE
42
LAB RESULT OF PX WITH HS
DAT- NEGATIVE MCV NORMAL TO LOW MCH- NORMAL MCHC SLIGHTLY INCREASED
43
CONFIRMATORY TEST FOR HS DISEAE
EMA BINDING TEST
44
LARGER THAN NORMAL RED CELL WITH BLUISH TINGE
PLOYCHROMATOPHILIC ERYTHROCYTES
45
BLUISH TINGE IN POLYCHROMATOPHILIC ERYTHROCYTE IS CAUSED BY
THE PRESENCE OF RESIDUAL RNA
46
LARGE UMBER OF POLYCHROMATOPHILIC ERYTHROCYTE CAN BE FOUND IN
DECREASED RBC SURVIVAL HEMORRHAGE ERYTHROID HYPERPLASTIC MARROW
47
EARLIEST METHOD PROVIDED BY THE HEMATOOLOGY ANALYZER TO EMASURE RED CELL VARIATION
RDW-CV
48
WHAT CONDITION HAS THIS DECREASED MCV AND LITTLE OR NO ANISOCYTOSIS
ANEMIA OF CHRONIC INFECTION
49
WHAT CONDITION HAS THIS DECREASED MCV AND INCREASED ANISOCYTOSIS
IDA