MSK - blood

Question 1

MC SCA location in diaphysis

Answer 1

Proximal femur

Question 2

DDx of tibiotalar slant

Answer 2

JCA, SCA, hemophilia or Fairbank disease (MED)

Question 3

Are medullary infarcts common in Thalassemia

Answer 3

uncommon

Question 4

Describe marrow hyperplasia

Answer 4

Osteoporosis, diploic widening, calvarial thinning, hair-on-end

Question 5

Does occiput contain red marrow

Answer 5

No, hence no marrow hyperplasia here

Question 6

Radial changes are pre or post acial

Answer 6

Pre-axial

Question 7

Bone infarcts occur in SCA or thalassemia

Answer 7

SCA and SC HbC

Question 8

MC extramedullary MM location

Answer 8

nasopharync

Question 9

Will normal marrow enhance in kids

Answer 9

Mildly

Question 10

Lower T1SI in marrow to muscles is good or bad

Answer 10

Bad

Question 11

Erlenmeyer flask and osteonecrosis

Answer 11

Gaucher disease

Question 12

2 Findings in Gaucher that are no in Neimann-Pick

Answer 12

Osteonecrosis and lytic lesions

Question 13

Virtually diagnostic on histo of LCH

Answer 13

LCH contains inclusion bondies

Question 14

Where do NHL vs HD occur

Answer 14

NHL = appendicular (LE - 40% knee)
HD = Axial

Question 15

Periostitis is prominent in NHL or HD

Answer 15

HD

Question 16

Cell in Hodgkin disease

Answer 16

Ree-Sternberg

Question 17

Classic location of Burkitts lymphoma

Answer 17

Facial bones

Question 18

Castleman dz is known as and is benign or malignant

Answer 18

Angiofollicular lymphoid hyperplasia

Benign mediastinal adenopathy

Question 19

Sjogren Triad

Answer 19

Conjunctivitis, Xerostomia and RA/similar

Question 20

Hemophilia likes

Answer 20

Knees, ankles and elbow

Question 21

JCA location

Answer 21

Small joints of hands and wrist

Question 22

% of AVN following intracapsular hip Fx/hip dislocation

Answer 22

75%/25%

Question 23

% of AVN scaphoid

Answer 23

15

Question 24

Do anemias spare skull bases

Answer 24

Yes. No red marrow

Question 25

Are facial bones spared in SCA

Answer 25

mandible

Question 26

Age of sickle cell dactylitis

Answer 26

6mo to 2 yrs

Question 27

Extramedullary hematopoiesis is more common in SCA or thalassemia

Answer 27

Thalassemia

Question 28

MC blood disorder

Answer 28

SCA

Question 29

Anemia with preaxial changes

Answer 29

Fanconi's anemia with hypoplasia of thumb and scaphoid

Question 30

Fanconi syndrome

Answer 30

Proximal renal tubules, renal tubular acidosis and phosphate loss

Question 31

POEMS

Answer 31

Polyneuropathy, organomegaly, endocrinopathy, M-proteins and skin changes

Question 32

Waldenstrom macroglobinemia is AKA

Answer 32

Lymphoplasmacytic lymphoma

Question 33

Amyloid in MM and waldenstrom is primary or secondary

Answer 33

Primary - MM, Secondary in Waldenstrom

Question 34

Rash in Fabry

Answer 34

Deep red on lower body

Question 35

Rad findings of Erdheim-Chester

Answer 35

Increase density with coarsened trabecula, medullary sclerosis, thickened cortex, symmetrical

Question 36

Define Budd-Chiari

Answer 36

Occulion of hepatic veins seen in polycythemia vera

Question 37

Define Von Wildebrand dz

Answer 37

Factor 8 deficiency with platelet abnormalities. MC hereditary bleeding disorder

Question 38

Klippel-trenauney-Weber shows

Answer 38

Varicose veins, bone hypertrophy and cutenous hemangiomas in one extermity

Question 39

Park-Weber shows

Answer 39

Klippel-Trenauney-Weber with AV fistula

Question 40

kasabak-merrit shows

Answer 40

Papillary hemangiomas and extensive bruising