Peds

Question 1

Danazole

Answer 1

testosterone derviative w/ progestin effects

rx for endometriosis

Question 2

Gastroschisis

Answer 2

high afp on quad screen
immediate surgery required
usually isolated defect

Question 3

KUB of sigmoid volvulul

Answer 3

inverted U shape
copffee bean sign
very very rare in kids

Question 4

Fetal alcohol syndrome

Answer 4

smooth philtrum
thin vermillion border
small palpebral fissures
microcephaly

Question 5

Rx for club foot

Answer 5

stretching/ manipulation
serial cats
surgery if the above fails
start trx immediately

Question 6

Galactosemia deficiency

Answer 6

galactose-1-uridyl transferase

Question 7

Laryngomalacia

Answer 7

colapse of airway during inspiration

improves w/ laying down (prone)

Question 8

Vascular rings

Answer 8

vessel traps trachea
inspitory and expirtpory stridor

improves
with neck extension

Question 9

B1 deficiency

Answer 9

thiamine
beriberi or wernicke
neuro/psych s/s
often in etoh or rapid wt loss

Question 10

Renal tubular acidodis basics

Answer 10

defectn in either H excretion or bicarb absorption

presents as growth failure

high chloride and low serum bicarb on labs

Question 11

Long QT rx

Answer 11

propanolol

pacemaker

Question 12

b6 deficiency

Answer 12

irritability dermatitis
depression
stomatitis

risk for DVT and atherosclerosis

Question 13

Neonatal abstinence syndrome

Answer 13

infant withdrawal from opiates

high pitched cry
poor sleep 
tremor/ sz
sweating 
sneezing 
NVD, anorexia

Question 14

Most common pneumonia in CF in infants/ young kids

Answer 14

staph

Question 15

When is a direct coombs test positive

Answer 15

in autoimmune hemolytic anemia

Question 16

Rocky mountain spotted fever in kids

Answer 16

fever
vasculitis 
petechiae 
anemia
thrombocytopenia 
hematuria

Question 17

mullerian agenesis

Answer 17

normal breast/ hair/ ovary

absent uterus, cervix, upper vagina

Question 18

5-a- reductase deficiency

Answer 18

connot convert testosterone to DHT

46 XY

appear female at birth, become male at puberty

Question 19

McCune albright syndrome

Answer 19

precoucious puberty
pigmentation (cafe spots)
polyostotic fibrous dysplasia

Question 20

Tetrology murmur

Answer 20

• crescendo decrescendo systolic murmur

- single S2 (normal aortic, quiet pulmonic)

Question 21

Rx for localized impetigo

Answer 21

topical mupirocin

Question 22

ALL

Answer 22

• most common leukemia 2-10 yo
• lymphoblasts in smear
• ddx by 25% blasts in marrow
• • PAS / TdT stain

Question 23

Auer rods are specific for?

Answer 23

AML

Question 24

12 month mile stones

Answer 24

• walk
• 2 finger grasp
• mama, dada, + 2/3 words

Question 25

Classic VSD murmur

Answer 25

harsh, holosystolic | L lower sternum

Question 26

Test for intracranial bleed

Answer 26

CT without

Question 27

Rx for developmental dysplasia of the hip

Answer 27

- clunk or asymmetric skin folds - ddx by US - best before 6 months - pavlik harness

Question 28

ringworm

Answer 28

FUNGUS- dermatophyte aka tinea corpis scaly, red, itchy

Question 29

Cholesteatoma in kids

Answer 29

new onset hearing loss chronic ear drainage granulation tissue/ skin debris

Question 30

lipid screening in kids

Answer 30

universal screening twice: 9-11 and 17-21

Question 31

rotovirus vaccine age

Answer 31

2-8 months

Question 32

meningococcal vaccine age

Answer 32

11-12 | booster at 16

Question 33

labs in common variable immunodeficiency

Answer 33

low immunoglobulin

Question 34

Kid with no tonsils or adenoids?

Answer 34

x linked agammaglobulinemia | brutons