U-World 4 Flashcards

(76 cards)

1
Q

What is refeeeding syndrome

A

Carbohydrate intake stimulates insulin activity, promoting cellular uptake of PO4, K, and Mg
arrythmias and cardiopulmonary failure

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2
Q

Two things to order when DiGeorge is suspected

A

Serum calcium levels and Ekg

Hypocalemia from hypoplasia of the parathyroid gland

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3
Q

Children who suffers from selective mutism are

A

verbal and talkative at home but refuse to speak in specific settings

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4
Q

2 finger vs 3 finger pincer grasp development

A

3 fingers at 9 months

2 fingers at 1 year

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5
Q

Height and weight in first year

A

Weight should triple and height should increase by 50%

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6
Q

Complex partial seizure features

A

Brief episodes of impaired consciousness, failure to respond to stimuli during episodes, starting spells, and post-ictal confusion

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7
Q

Next step in girl with primary amenorrhea if FSH is decreased

A

pituitary MRI

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8
Q

Workup for all children with recurrent episodes of nocturnal vulvar itching

A

Examined for pinworms and treated empirically with mebendazole

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9
Q

HSP leads to increased risk of

A

ileo-ileal intussusception

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10
Q

Chronic constipation is a risk factor for what in toddlers

A

Recurrent cystitis

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11
Q

Treatment of clubfoot

A

Stretching and manipulation of the foot followed by serial casts

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12
Q

Pertussis ppx for contacts of sick

A

Macrolides (only azithro for those under 1 month)

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13
Q

KUB for jejunal atresia

A

‘Triple bubble’ and gasless colon

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14
Q

what is used for CF sweat test

A

quantitative pilocarpine iontophoresis makes them sweat

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15
Q

Loss of cognitive functions post meningitis due to

A

Neuronal loss in the dentate gyrus of the hippocampus

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16
Q

Postexposure rabies prophylaxis

A

Rabies Ig and vaccine

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17
Q

Features of hereditary angioedema

A

Rapid onset of edema of the face, acral extremities, genitals, trachea, and abdominal organs without urticaria
C1 inhibitor def

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18
Q

Who should get varicella Ig

A

Immunocompromised hosts who are asymptomatic and non-immune

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19
Q

Most common Ewing’s sarcoma sites

A

Metaphysis and diaphysis of femur, followed by tibia and humerus

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20
Q

Triad of cardiac tamponade

A

Distant heart sounds, distended jugular veins (or scalp veins in babies), hypotension

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21
Q

CXR of CHF

A

Increased pulmonary vascular congestion and interstitial edema

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22
Q

Bone age in centra precocious puberty

A

Advanced (greater than actual age)

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23
Q

NF1 and NF2 mutations

A

NF1: Neurofibromin on C 17
NF2: Merlin on C 22

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24
Q

NF1 most common brain tumor

A

Optic pathway glioma

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25
ADA def results in
SCID (T cell def for viral and fungal issues)
26
When do patients with genetic B cell def begin to develop recurrent infections
After passing 6 months of age
27
Lack of what predisposes pt to Giardia
IgA
28
Gonococcal eye infection tx
IV ceftriaxone
29
Chlamydial eye infection tx
Oral erythromycin (also good for chlamydia pneumonia)
30
Def of what leads to Pellagra
Niacin (vit B3) | *Diarrhea, dermatitis, dementia*
31
What can riboflavin def cause
Cheilosis, glossitis, seborrheic dermaatitis
32
How can B6 (cyanocobalamin def) cause thrombosis
By increasing serum homocysteine
33
2-5 years drawing
2- copies a line 3- copies a circle 4- copes a square 5- copies a triangle
34
First line Ab class for pertussis
Macrolides
35
Gold standard for HIV testing from birth to 18 months
PCR
36
Most viral meningitis cases in kids cause by
Echo and Coxsackievirus
37
Acid base status of Iron poisoning
Anion-gap metabolic acidosis
38
Angular cheilosis and glossitis seen with what def? CBC will show?
Riboflavin | CBC will show a normocytic anemia
39
What does the knee chest position in a Tet spell do
Increases systemic vascular resistance (to overpower pulmonary vascular resistance)
40
Large VSD murmur
Pansytolic loudest at left lower sternal border and diastolic rumble at the apex due to increased flow across the mitral valve
41
Pineal gland tumor symptoms
Limited upward gaze, bilateral ptosis, and bilateral lid retraction *Also symptoms of ICP*
42
Congenital hypothyroidism signs
Apathy, hypotonia, large tongue, abdominal bloating, and umbilical hernia
43
Meconium ileus is virtually diagnostic for? Features of
CF | Obstruction is at the ileum and is inspissated
44
Drugs for absence seizures
Ethosuximide or valproate
45
What are growing pains
Bilateral, lower extremity pains that occur at night in children 2-12 years old
46
Presentation of spherocytosis
Hemolytic anemia, jaundice, and splenomegaly
47
Spherocytosis mutation
Ankyrin mutation causing spectrin deficiency
48
Glomerular damage of HSP
Mesangial deposition of IgA
49
Cat bite tx
5 day course of amoxicillin/clavulanate
50
What should be done for any child with behavioral concerns
Hearing test
51
MCC of acute unilateral lymphadenitis? Best tx?
S. aureus, followed by GAS | Clinda is the drug of choice (for MRSA coverage)
52
Always consider what in any adolescent prescient with significant emotional or school changes
Substance abuse, sexual abuse, and pregnancy
53
Two big suggesters for retropharyngeal abscess
Inability to extend neck | Widened prevertbral space on X-ray
54
Retropharyngeal abscess bugs
Polymicrobial
55
First two steps for newborn with diaphragmatic hernia
Endotracheal intubation | Gastric tube to decompress stomach and bowel
56
Hep B risk for what renal disease
Membranous nephropathy
57
Study to evaluate injury in chemical ingestions
Upper GI endoscopy
58
Two types of breath holding spells? What is often associated with them
Cyanotic- crying followed by breath holding Pallid- minor trauma followed by LOC * Iron def anemia often seen with *
59
What should be suspected in Down syndrome pt's who present with upper motor neuron findings
Atlantoaxial instability (caused by excessive laxity in posterior transverse ligament)
60
Dx of fanconis anemia? symptoms
Chromosomal breaks on genetic analysis Congenital marrow failure, poor growth, macroctyic anemia *abnormal thumbs*
61
First step for workup in neonate with bilious emesis who is stable
Imaging (contrast enema)
62
Two turners heart defects
Coarctation of aorta | Bicuspid aortic valve
63
History of trauma to soft palate with foreign body can lead to
Internal carotid artery dissection
64
In SS, acute severe anemia with low or absent reticulocytes c/w?
Aplastic crisis
65
Serum labs of RTA? Tx?
low serum HCO3 and hyperchloremia (normal anion gap acidosis) Tx is oral bicarb replacement
66
Beckwith-Widedemann syndrome features
Macrosomia, macroglossia, hemihpyerplasia and abdominal wall defects
67
BWS newborns monitored for?risks later?
Monitored for hypoglycemia | Risk of Wilm's tumor and hepatoblastoma
68
Cri-du-chat syndrome mutation
Deletion of 5p
69
Edwards syndrome features
Microcephaly, prominent occupy, micrognathia, CLOSED FISTS AND ROCKER BOTTOM FEET
70
Reye's syndrome liver biopsy
Micro vesicular fatty infiltration and hepatic mitochondrial dysfunction
71
2 diseases you can see Reye's with
Aspirin use in setting of influenza or varicella infection
72
Reye presentation
Vomiting, agitation and irrational behavior progressing to lethargy, stupor,a dn restlessness
73
3 reasons GERD more common in babies
1. Shorter esophagus 2. Incomplete closure of LES 3. Greater time spent in supine position
74
Most important step after Guillain-Barre is diagnosed
Spirometry to measure pulmonary function (FVC especially)
75
CBC of pertussis
Lymphocyte-predominant leukocytosis
76
What is Diamond-Blackfan syndrome
Microcytic pure red cell aplasia associated with short stature, webbed neck, cleft lip, triangular thumbs