Idiopathic Pulmonary Fibrosis Flashcards Preview

Clin Med I - Pulmonary > Idiopathic Pulmonary Fibrosis > Flashcards

Flashcards in Idiopathic Pulmonary Fibrosis Deck (15):
1

Define idiopathic pulmonary fibrosis

- chronic, progressive fibrosing interstitial PNA

2

What is the cause of IPF?

- unknown

3

What is the MC restrictive lung disease?

- IPF

4

What is the pathogenesis of IPF?

- stimuli --> lung injury --> inflammation --> wound healing --> fibrosis/decreased ventilation

5

T/F: There is a cure for IPF.

- false, no stopping it, only slows the progression

6

What are the possible inciting agents/triggers?

- smoke
- pollutants
- dust
- viral infx
- GERD
- chronic aspiration

7

T/F: IPF has a poor prognosis with survival of 2-5 years from time of dx.

- True

8

What are the S&S of IPF?

- nonspecific (dyspnea and/or nonproductive cough)
- gradual onset

9

What will be pertinent findings in the hx of IPF?

- smoker
- progressive dyspnea
- non-productive cough
- constitutional sx
- travel
- HIV/TB

10

What will be present on PE in IPF?

- fine basilar inspiratory crackles
- clubbing
- increased S2 intensity of fixed split S2
- holosystolic tricuspid regurgitation
- pedal edema

11

What diagnostic test should be performed in IPF?

- CXR/CT
- PFTs
- Bx

12

What will PFTs show in IPF?

~everything is low except FEV1/FVC~
- decreased TLC & RV
- normal or increased FEV1/FVC
- decreased DCLO

13

What will be seen on CXR/CT in IPF?

- reticular opacities (honeycombing)
- ground glass opacities

14

T/F: Hypoxemia is always present in IPF.

- False

15

What is the tx of IPF?

- lung transplant
- manage complications
- smoking cessation
- vaccinations
- pulm rehab
- refer to dietician