Flashcards in Idiopathic Pulmonary Fibrosis Deck (15):
Define idiopathic pulmonary fibrosis
- chronic, progressive fibrosing interstitial PNA
What is the cause of IPF?
What is the MC restrictive lung disease?
What is the pathogenesis of IPF?
- stimuli --> lung injury --> inflammation --> wound healing --> fibrosis/decreased ventilation
T/F: There is a cure for IPF.
- false, no stopping it, only slows the progression
What are the possible inciting agents/triggers?
- viral infx
- chronic aspiration
T/F: IPF has a poor prognosis with survival of 2-5 years from time of dx.
What are the S&S of IPF?
- nonspecific (dyspnea and/or nonproductive cough)
- gradual onset
What will be pertinent findings in the hx of IPF?
- progressive dyspnea
- non-productive cough
- constitutional sx
What will be present on PE in IPF?
- fine basilar inspiratory crackles
- increased S2 intensity of fixed split S2
- holosystolic tricuspid regurgitation
- pedal edema
What diagnostic test should be performed in IPF?
What will PFTs show in IPF?
~everything is low except FEV1/FVC~
- decreased TLC & RV
- normal or increased FEV1/FVC
- decreased DCLO
What will be seen on CXR/CT in IPF?
- reticular opacities (honeycombing)
- ground glass opacities
T/F: Hypoxemia is always present in IPF.