Sickle Cell Anemia

Question 1

How is this condition inherited ?

Answer 1

A child receives the gene from both parents.

Question 2

How long do sickled RBCs live compared to normal RBCs?

Answer 2

6-20 days: normal is 120

Question 3

What does this put the pt at risk for ?

Answer 3

Anemia

Question 4

What test determines sickle cell

Answer 4

Hemoglobin- shows anemia

Sickle testing of blood

Question 5

The acute exacerbation of sickle cell anemia is called__

Answer 5

Sickle cell crisis or Vaso-occlusive crisis

Question 6

The most common cause ?

Answer 6

Dehydration

Question 7

This causes the SIckled blood to do what ??

Answer 7

Clot

Question 8

How do you treat a sickle cell crisis?

Answer 8

Hydrate with Oral and IV fluids

Give O2 to increase tissue perfusion

A blood transfusion maybe needed

Give pain meds - very painful

Question 9

During a sickle cell crisis which intervention is done first—do O2 or hydrate with IV FLUIDS?

Answer 9

Hydrate with IV fluids

Remember during a crisis the blood is clumped together , so the goal is to decrease the viscosity of the blood . O2 will not reverse the cause . It will only prevent more clumping

Question 10

Is this Autsomal trait recessive or dominant?

Answer 10

Recessive; most commonly seen in African American