Cystic Fibrosis

Question 1

In cystic fibrosis, the ____ or exocrine gland are affected

Answer 1

Mucous producing

Question 2

How cystic fibrosis abnormally change mucous gland secretions

Answer 2

The mucous will become thick and sticky and cause obstruction

Question 3

What are two systems most affected by cystic fibrosis

Answer 3

Respiratory-mucous get trapped in the lungs

Digestive -mucous blocks the pancreas and digestive enzymes making the absorption of nutrients very difficult

Question 4

What is the most accurate test for cystic fibrosis ?

Answer 4

Sweat test- chloride levels will be > 60

Question 5

What are the ways to diagnose cystic fibrosis?

Answer 5

1. ) chest X-ray
2. ) stool analysis
3. ) pulmonary function test

Question 6

How does poor absorption of fat in the digestive tract change the appearance of stool?

Answer 6

It cause steatorrhea

greasy, fouls smelling, pale stool

Question 7

_____ are given with each meal to help with the absorption of nutrients

Answer 7

Pancreatic enzymes

Question 8

What is the most important diet for cystic fibrosis?

Answer 8

High calorie, high protein , high fat

Question 9

______ is common technique used to clear thick mucous from the lungs . This is important for preventing respiratory infections.

Answer 9

Postural drainage

Question 10

What should parents who already have a child with cystic fibrosis do before having another child ?

Answer 10

They should get genetic counseling because cystic fibrosis is hereditary