Cystic Fibrosis Flashcards Preview

Peds Exam 2 > Cystic Fibrosis > Flashcards

Flashcards in Cystic Fibrosis Deck (25):
1

what kind of a disorder is this

autosomal recessive

2

which parts of the body does this affect

exocrine glands

3

what happens to secretions with this disease

abnormally viscous

4

what is required for a person to get this disease

2 copies of genes

5

which 2 organs are most affected

pancreas
lungs

6

which compound is unusually high in the body

sodium chloride

7

what are the 3 major presentations in infancy

meconium ileus
failure to thrive
chronic respiratory infection

8

what are the 2 major presentations in older children

fecal impaction
intussusception

9

what are 4 late symptoms

pulmonary hypertension
R ventricular failure
respiratory failure
death

10

what is normally seen as symptoms

non-productive cough
patchy atelectasis
clubbing
barrel chest

11

which 2 things are not digested properly

fat
protein

12

what is a major test in diagnosis

sweat analysis for high NaCl

13

which 4 absorption problems are commonly seen

hyponatremia
hypokalemia
hypoalbuminemia
alkalosis

14

what is the normal value for the sweat chloride test

< 40

15

what is the sweat chloride value for CF pts

> 60

16

at which value would you retest for the sweat chloride test

40-50

17

what should the hydration level be

1.5x normal

18

which classification of med should not be given

antihistamine

19

which 3 enzymes can be given

catazyM-S
Pancrease
Ultrace

20

what are 4 ways to maintain optimal fluid status

high calorie
high protein
increased fluids
enzyme supplements

21

what does lactulose prevent

distal intestinal obstruction

22

when should chest PT be done

1 hour before or 2 hours after meals
before bedtime

23

when should pancreatic enzymes be given

within 30 mins of eating

24

what is the worst complication

pseudomonas

25

what is another serious complication

cor pulmonale