Idiopathic Pulmonary Fibrosis (IPF) Flashcards Preview

Respiratory Diseases > Idiopathic Pulmonary Fibrosis (IPF) > Flashcards

Flashcards in Idiopathic Pulmonary Fibrosis (IPF) Deck (10)
Loading flashcards...
1
Q

what is it

A

imbalance in fibrotic repair system of lungs = lay down unrequired scar tissue
chronic inflammatory infiltrate (neutrophils) causes fibrosis in alveolar walls and macrophages

2
Q

what does it cause increased risk of

A

infection

3
Q

prevalence

A

more common in males

4
Q

causes

A

idiopathic

5
Q

secondary causes

A

rheumatoid, SLE, system scleorisis, asbestosis, drugs

6
Q

symptoms

A

progressive exertional dyspnoea

dry cough

7
Q

signs

A

clubbing
bibasal crackles on auscultation
dry cough

8
Q

diagnosis

A

CXR - bilateral infiltrates, fine inspiratory crackles
HRCT - bilateral lower zone fibrosis/shadowing - ground glass
restrictive PFT and low TLCO

9
Q

treatment

A
oral steroids 
immunosuppressants (azathioprine)
O2 if hypoxic 
pulmonary rehab 
lung transplant in young patients
10
Q

complications

A

respiratory failure

most patients dead in 5 years