Pediatrics: Special Forms of Strabismus Flashcards

0
Q

Goldenhar syndrome, Wildervanck syndrome

A

two syndromes associated with Duane syndrome

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1
Q

retraction on adduction, restricted horizontal eye movement, vertical shoots

A

three essential features of Duane syndrome

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2
Q

AD

A

though usually sporadic, 5-10% of cases of Duane syndrome are inherited in this manner

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3
Q

absence of the CN VI nucleus

A

MRI finding in Duane syndrome

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4
Q

type I

A

Duane syndrome with esotropia in primary gaze and primary abduction defect

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5
Q

type II

A

Duane syndrome with exotropia in primary gaze and primary adduction defect

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6
Q

type III

A

Duane syndrome with small heterotropia (or none) and marked limitation of both adduction and abduction

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7
Q

resection

A

type of surgery that is recommended against in Duane syndrome

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8
Q

deviation in primary position, head turn, large shoots, marked globe retraction

A

four indications for surgery in Duane syndrome

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9
Q

MR recession

A

typical surgery for type I Duane’s syndrome

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10
Q

LR recession

A

typical surgery for type II Duane’s syndrome

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11
Q

none

A

typical surgery for type III Duane’s syndrome

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12
Q

spontaneous resolution

A

Prominent feature of acquired Brown syndrome that is less common (though not entirely unusual) in congenital Brown syndrome

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13
Q

globe retropulsion

A

what maneuver will worsen restriction in Brown syndrome, in contrast to IR restriction?

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14
Q

primary gaze hypotropia, downshoot in adduction

A

two additional findings in severe Brown syndrome

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15
Q

intermuscular septum

A

In superior oblique tenotomy with spacer, care must be taken to repair this to prevent downgaze restriction

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16
Q

50%

A

percentage of cases of CN III palsy in children that are congenital

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17
Q

aberrant regeneration, miosis

A

two prominent features of congenital CN III palsy that help distinguish it from acquired

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18
Q

6 months

A

period of time that should be allowed to pass before performing strabismus surgery on a child with a cranial nerve palsy

19
Q

LR recession, MR resection, superior tendon transposition

A

usual surgery for CN III palsy

20
Q

LR disinsertion

A

option to treat CN III palsy with severe abduction

21
Q

SO tenotomy

A

option to correct hypotropia in CN III palsy

22
Q

50%

A

minimum percentage of patients with traumatic CN VI palsy with complete recovery

23
Q

MR recession, LR resection

A

surgical treatment of partial CN VI palsy

24
Q

hypotropia, esotropia

A

two most common deviations due to TED

25
Q

6 months

A

period of stability of muscle alignment in TED before considering strabismus surgery

26
Q

disinsertion of lower lid retractors

A

often incorporated into most common strabismus surgery for TED

27
Q

bilateral frontalis sling

A

main treatment option for CPEO

28
Q

EKG, DFE

A

should be investigated closely in any patient with CPEO

29
Q

Cogan twitch

A

term for overshoot of the eye on looking ahead after looking down for several minutes

30
Q

true

A

TRUE or FALSE: CPEO does not usually cause diplopia

31
Q

generalized, strabismus fixus, IR restriction, vertical retraction syndrome

A

four main variations of congenital fibrosis syndrome

32
Q

true

A

TRUE or FALSE: Mobius syndrome is commonly associated with limitations of adduction

33
Q

esotropia

A

form of strabismus caused by excessive axial length in myopia

34
Q

ipsilateral MR resection, contralateral LR recession

A

surgical treatment for INO

35
Q

ataxia-telangiectasia

A

phakomatosis associated with ocular motor apraxia

36
Q

ocular motor apraxia

A

condition characterized by head shoots followed by correction instead of normal saccades

37
Q

false

A

TRUE or FALSE: Superior oblique myokymia is associated with neurologic abnormalities and warrants neuroimaging

38
Q

retraction on adduction

A

finding in Duane syndrome that obviates a search for a neurologic cause of sixth nerve paresis

39
Q

75%

A

up to this percentage of cases of congenital Brown’s syndrome improve spontaneously

40
Q

CT orbits and paranasal sinuses

A

indicated in acute-onset Brown’s syndrome

41
Q

true

A

True or False: A true retinitis pigmentosa is unusual in cases of CPEO and Kearns-Sayre syndrome

42
Q

AD

A

more common inheritance pattern in CFEOM

43
Q

vertical retraction syndrome

A

term CFEOM of the SR primarily

44
Q

MR recession

A

main treatment for Mobius syndrome (should be done cautiously)

45
Q

horizontal

A

Which saccades are affected in ocular motor apraxia, vertical, horizontal, or both?

46
Q

SO tenectomy

A

surgical therapy for SO myokymia