18-6

Question 1

Choledochal cyst

Answer 1

Congenital dilation of common bile duct

Question 2

Congenital dilation of common bile duct

Answer 2

Choledochal cyst

Question 3

When/who do Choledochal cysts usually present in?

Answer 3

Female children

Question 4

Symptoms of Choledochal cysts?

Answer 4

Jaundice and abdominal pain

Question 5

Symptoms of Choledochal cysts?

Answer 5

Jaundice and abdominal pain

Question 6

Kids with Choledochal cysts are at an increased risk to develop what conditions?

Answer 6

Stone formation
Stenosis
Pancreatitis
Obstructive biliary issues

Question 7

What 3 things fall under the Fibropolycystic Disease category?

Answer 7

Von Meyenburg Complexes
Caroli Disease/Syndrome
Congenital Hepatic Fibrosis

Question 8

What 3 things fall under the Fibropolycystic Disease category?

Answer 8

Von Meyenburg Complexes
Caroli Disease/Syndrome
Congenital Hepatic Fibrosis

Question 9

Von Meyenburg Complexes

Answer 9

Bile duct hamartomas

Question 10

Bile duct hamartomas

Answer 10

Von Meyenburg complexes

Question 11

Caroli Disease

Answer 11

Multifocal cystic dilation of large intrahepatic bile ducts

Question 12

Multifocal cystic dilation of large intrahepatic bile ducts

Answer 12

Caroli Disease

Question 13

Caroli Syndrome

Answer 13

Multifocal cystic dilation of large intrahepatic bile ducts + Congenital hepatic fibrosis

Question 14

Multifocal cystic dilation of large intrahepatic bile ducts + congenital hepatic fibrosis

Answer 14

Caroli Syndrome

Question 15

Congenital hepatic fibrosis

Answer 15

Bands of collagenous tissue that form septa and divide the liver into islands

Question 16

Bands of collagenous tissue that form septa and divide the liver into islands

Answer 16

Congenital hepatic fibrosis

Question 17

Congenital hepatic fibrosis includes _____ shaped bile ducts imbedded in the fibrosis

Answer 17

Abnormally shaped bile ducts

Question 18

Those with Congenital hepatic fibrosis are at an increased risk for?

Answer 18

Portal HTN and bleeding varices

Question 19

Fibropolycystic Disease

Answer 19

Congenital malformations of the biliary tree

1. Von Meyenburg Complexes
2. Caroli Disease/Syndrome
3. Congenital Hepatic Fibrosis

Question 20

What causes Fibropolycystic Disease?

Answer 20

Ductal plate malformations due to the persistence of fetal periportal ductal plates

Question 21

What is associated with Fibropolycystic Disease?

Answer 21

Renal polycystic disease

– Increased risk for cholangiocarcinoma

Question 22

2 causes of Impaired blood flow into the liver?

Answer 22

1. Hepatic A. compromise

2. Portal vein obstruction

Question 23

Signs of Hepatic A. compromise?

Answer 23

Pale or hemorrhagic infarct of the liver

Question 24

Common causes of Hepatic A. compromise?

Answer 24

Neoplasia, polyarteritis nodosa, sepsis

Question 25

Symptoms of Portal vein obstruction?

Answer 25

Abdominal pain, portal HTN with ruptured esophageal varices

Question 26

Symptoms of Portal vein obstruction?

Answer 26

Abdominal pain, portal HTN with ruptured esophageal varices

Question 27

What can cause extrahepatic portal vein obstruction?

Answer 27

Idiopathic Umbilical vein catheterization Hypercoagulable states

Question 28

What usually causes small branch portal vein obstruction?

Answer 28

Schistosomiasis - parasites laying eggs that cause obstruction

Question 29

Schistosomiasis (parasites laying eggs) can cause?

Answer 29

Small branch portal vein obstruction

Question 30

Signs of small branch portal vein obstruction?

Answer 30

NONcirrhotic portal HTN

Question 31

NONcirhortic portal HTN

Answer 31

Small branch portal vein obstruction

Question 32

Most common cause of impaired blood flow through the liver?

Answer 32

CIRRHOSIS

Question 33

Most common cause of impaired blood flow through the liver?

Answer 33

CIRRHOSIS

Question 34

Besides cirrhosis, what is another condition where blood flow is impaired through the liver?

Answer 34

Peliosis Hepatitis

Question 35

Peliosis Hepatitis

Answer 35

Sinusoidal dilation where EFFLUX of hepatic blood is impeded

Question 36

Peliosis Hepatitis

Answer 36

Sinusoidal dilation where EFFLUX of hepatic blood is impeded

Question 37

What will the liver contain with Peliosis Hepatitis?

Answer 37

Blood-filled cystic spaces | -- sinusoidal dilation where EFFLUX of hepatic blood is impeded

Question 38

What conditions may cause Peliosis hepatitis?

Answer 38

AIDs - bartonella species Cancer TB Sex hormone administration

Question 39

2 causes of Hepatic venous outflow obstruction?

Answer 39

Hepatic vein thrombosis | Sinusoidal obstruction syndrome

Question 40

Hepatic vein thrombosis =

Answer 40

Budd-Chiari syndrome

Question 41

Symptoms of Hepatic Vein Thrombosis (budd-chiari syndrome)?

Answer 41

Abdominal pain, ascites, hepatomegaly

Question 42

Symptoms of Hepatic Vein Thrombosis (budd-chiari syndrome)?

Answer 42

Abdominal pain, ascites, hepatomegaly

Question 43

In what 2 settings can Sinusoidal obstruction syndrome occur?

Answer 43

1. Following allogenic HSC transplant | 2. Cancer pts on chemotherapy

Question 44

Symptoms of Sinusoidal obstruction syndrome?

Answer 44

Ascites, hepatomegaly, weight gain and jaundice

Question 45

Symptoms of Sinusoidal obstruction syndrome?

Answer 45

Ascites, hepatomegaly, weight gain and jaundice

Question 46

What will a doppler US see with Sinusoidal obstruction syndrome?

Answer 46

Reversed/attenuated hepatic venous flow

Question 47

Preeclampsia

Answer 47

Maternal HTN, proteinuria, peripheral edema and coagulation abnormalties

Question 48

Preeclampsia

Answer 48

Maternal HTN, proteinuria, peripheral edema and coagulation abnormalities

Question 49

Signs of Preeclampsia?

Answer 49

HELLP - Hemolysis - Elevated Liver enzymes - Low Platelets

Question 50

Signs of Preeclampsia?

Answer 50

HELLP - Hemolysis - Elevated Liver enzymes - LOW platelets

Question 51

Eclampsia

Answer 51

Maternal HTN, proteinuria, peripheral edema, coagulation abnormalities + Hyperreflexia and convulsions

Question 52

Eclampsia

Answer 52

Maternal HTN, proteinuria, peripheral edema, coagulation abnormalities + Hyperreflexia and convulsions