Cystic Fibrosis Flashcards Preview

Pass Naplex Now Book II > Cystic Fibrosis > Flashcards

Flashcards in Cystic Fibrosis Deck (11):
1

Malnutrition is common in CF, how to manage it

Management
- High calorie diet
- Vit supplement: ADEK
- Pancreatic enzymes

2

Tobi

- Dose/frequency
- Indication

Tobromycin

- 300mg Neb BID 28d on and 28d off
- CF Chronic pseudo colonization

3

Dornase alpha

- MOA
- Indication
- Dose
If also on Tobi, give which one first
- Age
- Neb use:

Pulmonzyme

- MOA: mucolytic
- Indication: CF
- Dose: 1 amp by INH QD. Do not mix w/ other nebulizer
If also use w/ Tobi, use dornase alpha first.
- Age: > 6 y.o
- Neb: Pari LC jet Nebulizer

4

Creon

- Contain
- Time of administration
- Counseling

Pancreatic enzymes

- Contain: amylase, lipase, proteinase
- Taken just b/4 meals and snacks

Counseling
- Avoid Ca carbonate and Mg: effect coating of beads
- Do not chew/crush
- Take w/ liquid and swallow whole
- May mix in small amt of soft food
- Avoid mix w/ milk base foods
- do not mix enzymes into foods ahead of time
- Keep enzymes at RT
- Do not fridge
- Do NOT accept generic
- Enzymes are needed with all meals and snacks
- Some foods and drinks do not require enzymes b/c they contain only simple carbo that digest easily.

5

Pancrease

Pancreatic enzyme

6

Pancrecarb

Pancreatic enzyme

7

Ultrase

Pancreatic enzyme

8

Viokase

Pancreatic enzyme

9

Cayston

- Form:
- Indication
- Frequency
- Storage

Aztreonam

- Form:
- Indication: CF chronic pseudo colonization
- Frequency: 750 mg INH TID 28 days on and 28 days off
- Store in fridge.
RT ok for 28d.
Protect from light

10

Kalydeco

- Indication
- Age

Ivacaftor

- CF pt with G551D mutation
- Age: > 6 y.o

11

Hypertonic saline

- Indication
- SEs

- CF
- ADEs: cough, sore throat, chest pain, tissue irritation