kef 39 ,diataraxes n/m sinapsis Flashcards Preview

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Flashcards in kef 39 ,diataraxes n/m sinapsis Deck (13)
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1
Q

i d penikillamini antimetwpizei tin r.a tin noso wilson kai tin kistinouria alla ti prokalei kai sifili

A

anaptisei antiswmata kata tou achR => defteropathi miastheneia

2
Q

i anevresi anti AchR antiswmatwn ti apokliei?

A

tin iparksi siggwnwn miasthenikwn sindromwn

3
Q

ti kanei i miastheneia

A

kimainomeni adinamia miwn i omadwn miwn pou epiteinete me tin prospatheia kai ifiete kata tin ksekourasi kai tin lipsi antixolinesterasikwn ,50% ekdilwsi me prsvoli ofthalmikwn miwn me diplwpia kai asimmetri ptwsi vlefarou, simeio klidarotripas se klista matia giati fenete o skliros , oxi entoni gimnastiki , otan anevasoume to pathologiko vlefaro to fisiologiko paei pio katw

4
Q

klimakwsi miastheneias

A

diplwpia ptwsi vlefarou,amimia proswpou,adinamia masitirwn ,diataraxes kataposis kai fonis,prosvoi miwn akrwn ,anapnevstika mies spania(ta tenontia antanaklastika diatirountai kai den iparxoun aisthitikes diataraxes)

5
Q

pathofisiologia miastheneias

A

aftoanoso kata ipodoxewn ach

6
Q

diagnwstikoi methodoi miastheneias

A

dokimasia anastoleis tis achesterasis (tensilon neostigmini)
ipies metavoles sto ilektromiografima miopathitikou tipou kai emfanisi grigoris kopwsis kai o epanaliptikos erethismos meiwnei to dinamiko enrgeias ,anti achr antiswmata ston oro, ct gia thimwma

7
Q

therapeia miastheneias

A

anastoleis xolinesterasis:neistigmini piridostigmini aftes kanoun parenergeies naftua emetos sielorroia diarroia kai antimetwpizontai me atropini, thimektimi ,kortikosteroeidi prednizoni eiwnoun drasi b lemf ,azatheiprini kai kiklospirini ,plasmafairesi (anti AchR) andoflebia xorigisi anososgairinwn

8
Q

miastheniki xolinergiki krisi

A

otan den mporoun ta farmaka na to antimetwpisoun kanei miastheniki kai paralioun oi anapnevstikoi mies ,otan iparxei avksimeni posotita xolinergikwn tote exoume ekpolwtiko apokleismo ipodoxewn apo ipedosologia ……kanoume plasmaferesi gia pio taxeia apokatastasi

9
Q

sindromo lamber eaton pathofisiologia

A

epiktito aftoanoso stou antres kiriws,2/3 mazi me neoplasma ,1/3 mazi me alla aftoanosa ,meiwsi diavlwn ca epomenos kathisterisi apeleftherwsis ach logo drasis aftoantisomatwn.

10
Q

lamber eaton kliniki eikona

A

..klinika exoume kormiki kai kentromieliki adinamia ,se epanalamvanomeno erethismo exoume prosorini dinami ,meiwnountai ta tenontia antanaklastika exoume simptwmata apo to aftonomo, ksirostomia ( mouslarinikes apolimseis)

11
Q

diagnwsi lamber aeton

A

anastoleis achE ftwxa ,se tetaniko erethismo exoume aksisi fisiologikou ipsous dinamikwn!!!! enw se epanalamvanomena exoume araiwsi

12
Q

therapeia lamber aeton

A

antimetwpisi ipokeimenis kakoitheias ,3,4 aminopiridini me piridostigmini,anosokatastaltika prednizoni azatheiprini psasmaferesi kai anososfairines

13
Q

se miastheneia poia farmaka antedeiknintai

A

aminoglikosidi , kinolones , b blocker