kef 30 pathiseis periferikou ns Flashcards Preview

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Flashcards in kef 30 pathiseis periferikou ns Deck (31)
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1
Q

ti einai i baleriani ekfilisi

A

ekflisisi twn nevraksonwn twn nevrikwn kitarwn

2
Q

xaraktiristiki okseia/ipokseia nevropatheia

A

guillain barre

3
Q

kinitikes nevropatheies

A

guillain barre(flegmwnwdi apomielinwtiki) ,porfiria diftheritida kai molivdo

4
Q

aisthitikes nevropatheies

A

apo lepra ,sd(aksoniki nevropatheia),amiloeidwsi ,elleipsib12(aksoniki nevropatheia)

5
Q

sti nevroapraksia exoume _ enw stin aksonotmisi exoume_

A

tmimatiki apomielinwsi pou nevrou logo piesis,,,,,,,aksoniki ekfilisi(se oliki fasi nevronotmisi)

6
Q

poio nevro perna apo ton tarsiaio solina kai poies oi kiries diakladwseis tou

A

to knimiaio/…. esw kai eksw pelmatiaio ,

7
Q

peroniaia miiki atrofia nosos cmt i klironimiki kinitiki kai aisthitiki nevropatheia(hmsn)

A

provlima stin mielini(gonidia pmp-22,po) epomenos apomielinwsi,atrofia sta katw akra podia pelargou kai koilopodia

8
Q

oikogeneis amiloeidikes polinevropatheies

A

epodines paresthisies sta katw akra,apoleia mikrwn aisthitikwn nevrwn prwta (thermokrasias kai ponou),meta diataraxi se ola ta oidi periferikwn nevrwn,(diataraxes aftonomou,provlima sta gonidia amiloeidikwn prwteinwn: transthiretinis(ttr) ,apolipoprwteini a1,gkelsonini

9
Q

33% twn asthenwn 1-4 vdomades prin tin gb emfanizoun loimwksi apo poia mikrovia einai?

A

kampilovaktiridio tis nistidos(diarroiko sindromo),cmv,ebv,mikoplasma tis pnevmonias,ipatitida,hiv

10
Q

pathan vlavi guillain barre(okseia flegmwnwdis apomielinwtiki polirizonevropatheia)

A

diaxiti poliestiaki tmimatiki apomielinwsi se ola ta periferika nevra ,sto simeio tis apomielinwsis exoume lfegmonwdi diithisi apo lemfokitara kai sto telos aksoniki ekfilisi

11
Q

simtwmata gb

A

okseia nevromiiki paralisi,aniousa proodeftiki miiki adinamia mexri ofthalmokinitikous ,apo ta katw akra mexri ton avxena,,katargisi tenwntiwn antanaklastikwn apo tis prwtes imeres, paraisthisies kai mialgies

12
Q

ergastiriaka evrimata gb

A

leukomatokittarikos dixasmos so eny(avksimeno lefkwma,fisiologika kittara),se ilektrofisiologiko elegxo exoume meiomeni taxitita agwgis k F kimma se eksetaseis aimatos exoume: antiswmata kata gaggliosidwn GM1 (25% twn periptwsewn),tke,lefka,ipatika ,meiwsi na(provlima stin antidiouritiki)

13
Q

klinikes parallages gb

A

sindomo miller fisher(ekswteriki ofthalmopligia ataksia kai katargisi tenontiwn antanaklastikwn) : ston oro IgG enanti gaggliosidiou GQ1b ,

14
Q

poreia gb

A

egkatastasi 1-4 w
statheropoisi 2-4 w
apokatastasi 6m -2y

15
Q

therapeia gb

A

plsamaferesi 2-4 siedries

iv anososfairini 0,4g/kg gia 5d

16
Q

xronia flegmonwdis apomielinwtiki polirizonevropatheia CIDP ,poia einai ta ipoxrewtika klinika kritiria diagnwsis

A

proodeftiki miiki adinamia(>2 months)
meiwsi i katargisi antanaklastikwn
miiki adinamia kai periferika aisthitika simptwmata

17
Q

xronia flegmonwdis apomielinwtiki polirizonevropatheia,ergastiriaka (therapeia ;prednizoni kai plasmaferesi)

A

prwteini eny >45mg/ml kai kittara therapeia prednizoni

18
Q

poies nosoi kanoun paraprwteinemia(avksisi monoklwnikou antisomatos dld anososferines apo plasmatokitara)

A

mielwma,lemfwma,makrosfairinaimia ,sistimatiki amiloeidwsi,aftes oi paraprwteines Ig(M–>MAG,G,A) exoun antigona stoxous

19
Q

poreia makrosfairinaimias tou waldenstrom

A

kakoithi lemfokittara ston mielo ,ekrinoun igM monoklwniki prwteini , afti kanei vareia simmertriki aisthitiki nevropatheia (paraisthisies algos +krampes ,anti MAG drastiriotita

20
Q

prosvoli periferikou nevrikou ti exoume me poiu katastrofi

A

katastrofi kitarikou swmatos:nevrwnopatheia eite kinitiki(prwsthio keras) eitai aisthitiki(nwtiaio gagglio) ,..aksonikes nevropatheies vlavi stous nevraksones kinitikous i aisthitikous….apomielinwtikes nevropatheies elitro mielinis schwann–>parempidisi agwgimotitas miiki adinamia ipies diataraxes aisthitikotitas (meiwsi taxititas agwgis)…meiktes nevropatheies(aksoniki ekfilisi tmimatiki apomielinwsi)

21
Q

nevropatheies aksonikes

A

idiopathis,metabolikes :diavitiki ipothireoeidiki nefriki aneparkeia ,toksikes ,steritikes alkool b12 e, sistimatikes sarkoeidwsi likos ,paraprwteinaimikes paraneoplasmatikes

22
Q

nevropatheies apomielinwtikes

A

FLEGMONWDEIS gb cidp poliestiaki kinitiki nevropathiea paraprwteinaimikes KLIRONOMIKES cmt t1 kai tipou 2 TOKSIKES,MITOXONDRIAKES,LOIMWDEIS ,LEMFWMA

23
Q

polinevropatheia :

A

simmetriki prosvoli twn periferikwn nevrwn apo toksikes metavolikes i klironomikes astheneies….ekfrazete eitai periferikou tipou (ganti kaltsa ) eitai kentromielikou tipou

24
Q

ti mporei na kanei pagidevsi nevrou

A

ipothireieidismos ,akromegalia ,arthropatheies ,kai katastaseis me genikevmeno eidima

25
Q

aisthitikokinitikes nevropatheies

A

sd ,nefriki aneparkeia alkoolismo ipith

26
Q

aftonomes nevropatheies

A

diaviti + prwima stadia amiloeidwsis

27
Q

sindromo karpiaiou solina logoi:(nevropatheia apo pagidevsi)

A

topiki pathologiki diergasia : travma ,lipwma kisti osteorthritikes alloiwseis ,se sxesi me sistimatikes katastaseis :egkimosini ipoth,akromegalia ,amiloeidwsi , idiopathes

28
Q

kliniki eikona sindromo karpiaiou solina

A

ponos kai paresthisies 3 prwtwn daktilwn kai palamis,mporei na antanakla kai kentrikotera,ipoxoroun me kremasma kai tinagma xeriwn,miiki adinamia atrofia ipaisthisia

29
Q

poio nevro kanei paraisthitiki miralgia

A

to eksw dermatiko nevro tou mirou

30
Q

sindromo tarsaiou swlina

A

dialeiponta kavstika algi stis patouses, aimwdies ,ipaisthisia

31
Q

avxeniki plegmatopatheia

A

prokaleitai apo ogkous pnevmona agkeiaka (s.d) toksika i aktinovolia,kanei pono ipaisthisia kai meiwsi kinitikotitas stin perioxi pou nevrwnei