Pathology of Renal Tumours Flashcards Preview

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Flashcards in Pathology of Renal Tumours Deck (18):
1

What is agenesis?

absence of one or both kidneys

2

What is hypoplasia?

small kidneys but normal development

3

What are horseshoe kidneys?

fusion at either pole, usually lower

4

What is cystic disease?

different from polycystic! simple cysts, very common, usually no functional disease

5

What is the infantile type of polycystic disease?

ARPKD

6

In which type of polycystic disease is there distortion of the reniform shape?

ADPKD

7

What is ARPKD associated with?

congenital hepatic fibrosis

8

What is the most common form of congenital cystic disease?

ADPKD

9

Where is the defect in PKD1?

chromosome 16

10

Where is the defect in PKD2?

chromosome 4

11

How does ADPKD usually present?

in adult middle life
with abdominal mass, haematuria and hypertension

12

What type of renal englargement occurs in ADPKD?

MASSIVE

13

What is ADPKD associated with?

Berry aneurysms in circle of Willis - subarachnoid haemorrhage

14

Name the common benign tumour which is white and has medullary origin.

fibroma

15

Describe a renal adenoma.

yellowish, in cortical region

16

What is an angiomyolipoma?

tumour which is a mix of fat, muscle and blood vessels

17

What is angiomyolipoma associated with?

tuberous sclerosis

18

What is JGCT?

tumour with production of renin,
causing secondary hypertension