25. Hereditary hemorrhagic telangiectasia.

Question 1

Definition of Hereditary Hemorrhagic Telangiectasia

Answer 1

• Rare genetic disorder
• Capillaries and small vessel dysplasia

Question 2

Etiology of Hereditary Hemorrhagic Telangiectasia

Answer 2

Gentic

Question 3

Clinical featues of Hereditary Hemorrhagic Telangiectasia

Answer 3

• Located tip and dorsum of tongue, lips
• Less frequently-buccal mucosa, palate and gingiva
• Bleeding from oral lesions after friction(can be vigorous)

Question 4

Diagnosis of Hereditary Hemorrhagic Telangiectasia

Answer 4

Histopathologic examination

Question 5

Differential diagnosis of Hereditary Hemorrhagic Telangiectasia

Answer 5

• Varicosities
• Multiple hemangiomas
• CREST syndrome

Question 6

Treatment of Hereditary Hemorrhagic Telangiectasia

Answer 6

Supportive-no specific treatment