[7] Cyanotic Congenital Heart Disease Flashcards Preview

[OS 213] CVS Module > [7] Cyanotic Congenital Heart Disease > Flashcards

Flashcards in [7] Cyanotic Congenital Heart Disease Deck (30):
1

Most common congenital heart disease?

Ventricular Septal Defect

2

Main Etiology for CHD

Idiopathic (Probably multifactorial)

3

Noted infection that causes Patent Ductus Arteriosus and Peripheral Pulmonary Stenosis

Rubella

4

Normal O2 Saturation on the Right Side of the Heart

75

5

Clinically Apparent O2 Saturation of Cyanosis

< 85%

6

How much reduced Hg to detect Cyanosis?

> 5 gm/dL

7

Clinical Features of Tetralogy of Fallot

Progressive Cyanosis
Retarded Growth NOT Mental Development

8

Why do children with ToF often squat?

To improve pulmonary blood flow

9

What are the Malformations of the Tetralogy of Fallot

1. Ventricular Septal Defect
2. Pulmonary Stenosis
3. Dextroposition of Aorta
4. Right Ventricular Hypertrophy

10

Describe the murmur present in ToF

Systolic Ejection Murmur

11

Most severe spectrum of ToF

Presents with Pulmonary Atresia

12

Least severe spectrum of ToF

Pink ToF

13

Proper Squat Form to Relieve ToF

Knee Chest Position

14

What does the body do to try to compensate for the Cyanosis?

Polycythemia

Because it thinks you need more Hb in the body, but that doesn't do anything

15

Why are patients with ToF prone to brain abscess?

Since you have virtually a single ventricle, when you have bacteria (usually coming from the dental flora) it can go from RV -> LV and instantly enter systemic circulation

Since the carotids are straight, it can go straight to the brain

16

Medical Management of ToF

Prevent Fe deficiency
Phlebotomy
Propanolol for Hypoxic Spells

17

Surgical Management of ToF

Palliative: Shunts (Blalock-Taussig Shunt, Central)
Definitive: VSD Closure
Infundibulectomy
Transannular Patching

18

Describe Murmur of Transposition of Great Arteries (TGA)

Single loud S2

Soft Systolic Murmur

19

Describe the shape of the heart in TGA

Egg-Shaped

20

Natural History of TGA w/o Intervention

Death

21

How do patients survive TGA?

If they have a VSD or PS

22

Palliative Care of TGA

Prostaglandin Infusion

Create interatrial communication

23

Definitive Care of TGA

Atrial Switch: Senning or Mustard Procedure

Arterial Switch: Jantene Procedure

24

Wall to Wall Heart is Characteristic of?

Ebstein's Anomaly

25

What do you need when you have Pulmonary Valve Atresia to survive?

Tricuspid Regurgitation
Patent Ductus Arteriosus
Atrial Septal Defect

26

What kind of blood is in the Right Atrium in Total Anomalous Pulmonary Venous Return?

All of it, oxygenated and non-oxygenated

27

Requirement of TAPVR for Survival

Atrial Septal Defect
Patent Foramen Ovale

28

What type of TAPVR is considered an emergency for neonates

Infracardiac TAPVR

29

Requirements of Hypoplastic Left Heart Syndrome

Atrial Communication
PDA big enough to support descending and ascending aorta

30

Describe Murmur of Truncus Arteriosus

Loud S2
Diastolic murmur at the Left Upper Sternal Border