Flashcards in  Cyanotic Congenital Heart Disease Deck (30):
Most common congenital heart disease?
Ventricular Septal Defect
Main Etiology for CHD
Idiopathic (Probably multifactorial)
Noted infection that causes Patent Ductus Arteriosus and Peripheral Pulmonary Stenosis
Normal O2 Saturation on the Right Side of the Heart
Clinically Apparent O2 Saturation of Cyanosis
How much reduced Hg to detect Cyanosis?
> 5 gm/dL
Clinical Features of Tetralogy of Fallot
Retarded Growth NOT Mental Development
Why do children with ToF often squat?
To improve pulmonary blood flow
What are the Malformations of the Tetralogy of Fallot
1. Ventricular Septal Defect
2. Pulmonary Stenosis
3. Dextroposition of Aorta
4. Right Ventricular Hypertrophy
Describe the murmur present in ToF
Systolic Ejection Murmur
Most severe spectrum of ToF
Presents with Pulmonary Atresia
Least severe spectrum of ToF
Proper Squat Form to Relieve ToF
Knee Chest Position
What does the body do to try to compensate for the Cyanosis?
Because it thinks you need more Hb in the body, but that doesn't do anything
Why are patients with ToF prone to brain abscess?
Since you have virtually a single ventricle, when you have bacteria (usually coming from the dental flora) it can go from RV -> LV and instantly enter systemic circulation
Since the carotids are straight, it can go straight to the brain
Medical Management of ToF
Prevent Fe deficiency
Propanolol for Hypoxic Spells
Surgical Management of ToF
Palliative: Shunts (Blalock-Taussig Shunt, Central)
Definitive: VSD Closure
Describe Murmur of Transposition of Great Arteries (TGA)
Single loud S2
Soft Systolic Murmur
Describe the shape of the heart in TGA
Natural History of TGA w/o Intervention
How do patients survive TGA?
If they have a VSD or PS
Palliative Care of TGA
Create interatrial communication
Definitive Care of TGA
Atrial Switch: Senning or Mustard Procedure
Arterial Switch: Jantene Procedure
Wall to Wall Heart is Characteristic of?
What do you need when you have Pulmonary Valve Atresia to survive?
Patent Ductus Arteriosus
Atrial Septal Defect
What kind of blood is in the Right Atrium in Total Anomalous Pulmonary Venous Return?
All of it, oxygenated and non-oxygenated
Requirement of TAPVR for Survival
Atrial Septal Defect
Patent Foramen Ovale
What type of TAPVR is considered an emergency for neonates
Requirements of Hypoplastic Left Heart Syndrome
PDA big enough to support descending and ascending aorta