HIRSCHSPRUNG DISEASE Flashcards
(16 cards)
other name for hirschsprung disease
congenital anganglionic megacolon
*Absence of parasympathetic ganglionic cells in a segment of the
colon (usually distal end of the intestine).
* Lack of nerve innervations leading to lack of, or alteration in,
peristalsis in the affected part.
hirschsprung disease
causes of HD
commonly exist with other congenital anomalies (usually down’s syndrome / trisomy 21) and anomalies of the urinary tract
clinical minfestation
- cant pass stool
- liquid / RIBBON stools
- fecal vomiting
- irritability / lethargy
- FTT, DHN
- distended abdomen, palpable stool masses
diagnostic tests
- barium enema x- ray
- Rectal manometry
- Rectal biopsy
an X-ray procedure used to visualize the large intestine (colon and rectum) by using a contrast material called barium
barium enema x- ray
a diagnostic test that measures the pressures within the anus and rectum to assess the function of the anorectal sphincter muscles
Rectal manometry
a procedure where a small tissue sample is taken from the rectum for examination
Rectal biopsy
pre-op mgmt
- daily colon lavage
- digital exam
- anitbiotics
residual pouch of aganglionic bowel left intact with the healthy bowel attached behind
duhamel
the outer layer of the aganglionic bowel is left in place (muscular cuff)
soave
all of the aganglionic bowel is removed
swenson
treatment
colostomy and ileostomy
creates an opening (stoma) in the abdomen, allowing waste to exit the body through a pouch or bag
ostomy
what do you need to WOF
enterocolitis
s/sx of enterocolitis to WOF
- fever
- swollen abd
- vomiting
- diarrhea
- rectum bleed
- sluggishness
