Flashcards in Vasculitides Deck (39)
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31
Microscopic polyangiitis bx?
- Necrotizing vasculitis in lungs, kidneys, skin
- Pauci-immune GN
- Palpable purpura
- NO GRANULOMAS
32
Microscopic polyangiitis marker?
p-ANCA (MPO-ANCA) - anti-myeloperoxidase
33
Microscopic polyangiitis rx?
Cyclophosphamide, corticosteroids
34
Churg-Strauss (eosinophilic granulomatosis with polyangiitis) presentation?
Asthma, sinusitis, skin nodules/purpura, peripheral neuropathy (wrist/foot drop)
35
Churg-Strauss (eosinophilic granulomatosis with polyangiitis) bx?
Granulomatous, necrotizing vasculitis with eosinophilia
36
Churg-Strauss (eosinophilic granulomatosis with polyangiitis) marker?
p-ANCA, increased IgE
37
Henoch-Schonlein purpura presentation?
KIDS, follows URI
- Skin: palpable purpura on buttocks/legs
- Arthralgias
- GI: abdominal pain and bleeding
38
Henoch-Schonlein purpura pathogenesis?
IgA immune complex deposition
Type III HSN
39