peds103

Question 1

diff between umbilical hernia, oomphalocele, and gastroschesis

Answer 1

umbilical hernia covered by skin, oomphalocele covered by peritoneaum, gastroschesis uncovered intestines (always to the right)

Question 2

simple febrile seizure

Answer 2

nonfocal (tonic-clonic or atonic), one episode less than 15 mins or multiple less than 30 mins

Question 3

complex febrile seizure

Answer 3

focal, one episode greater than 15 mins or multiple greater than 30 mins

Question 4

management of febrile seizure

Answer 4

abortive therapy if seizure greater than 5 mins, reassurance/education; brain imaging can be considered in complex febrile seizure only

Question 5

prognosis for febrile seizures

Answer 5

normal development/intelligence; 30% risk of recurrence, less than 5% risk of epilepsy

Question 6

age for febrile seizures

Answer 6

6 mos to 6 years

Question 7

recurrent URI, persistent nasal drainage, and nasal polyps

Answer 7

rule out CF

Question 8

2 yo how many words

Answer 8

200 words

Question 9

builds a tower of 6 cubes

Answer 9

2 years

Question 10

walks down and up stairs, jumps, throws a ball overhead

Answer 10

2 years

Question 11

follows two step commands, removes clothes

Answer 11

2 years

Question 12

copies a circle, uses utensils, stacks 9 blocks

Answer 12

3 yo

Question 13

climbs stairs with alternating feet

Answer 13

3 yeas

Question 14

rides a tricycle

Answer 14

3 years

Question 15

states first name

Answer 15

3 yo

Question 16

washes/dries hands

Answer 16

3 yo

Question 17

draws a person, begins to use sciessors, holds crayon with tripod grasp

Answer 17

4 yo

Question 18

hops on one foot without losing balance

Answer 18

4 yo

Question 19

counts to 10

Answer 19

4 yo

Question 20

tells stories, uses plurals and prepositions

Answer 20

4 yo

Question 21

klumpke palsy

Answer 21

c8, t1 are injured; forearm pronators, wrist flexors, and dilators of the iris and elevators of the eyelid ; claw hand; moro intact; grasp reflex absent

Question 22

erb-duchenne palsy

Answer 22

most common type of brachial plexus injury and involves the C5 and C6; leads to waiter’s tip posture; grasp reflex intact; may have decreaed or absent moro reflexes

Question 23

newborn with failure to thrive, bilateral cataracts, jaundice, and hypoglycemia

Answer 23

galactosemia, caused by galactose-1-phosphate uridyl transferase def, leading to elevated galactose in the blood

Question 24

aminoaciduria, hepatic cirrhosis, hypoglycemia, and mental retard

Answer 24

galactosemia

Question 25

neonate with cataracts only

Answer 25

galactokinase def

Question 26

neonate with cutaneous lesions on the palms and soles, hepatosplenomegaly, jaundice, anemia, and rhinorrhe

Answer 26

congenital syphilis

Question 27

late congenital manifestations of syphilis

Answer 27

present after two years of age; frontal bossing, high arched palate, hutchinson teeth, intersitialkeratitis, saddle nose, and perioral fissures

Question 28

treatment for syphilis

Answer 28

parenteral penicillin G

Question 29

hepatosplenomegaly, hydrocephalus, chorioretinisit, and intracranial calcifications

Answer 29

congenital toxo

Question 30

sensorineural hearing loss, cataracts, heart defects, hepatosplenomegaly, petechiae or purpura (blueberry muffin)

Answer 30

congenital rubella

Question 31

IUGR, hepatosplenomegaly, petechiae or purpura, microcephaly, chorioretinitis, sensorineural hearing loss, and periventricular calcifications

Answer 31

congenital CMV

Question 32

xray of baby born with congenital syphilis

Answer 32

metaphyseal dystrophy and periositis

Question 33

fever, odynophagia/dysphagia, drooling, neck siffness, muffled voice, and unable to open the mouth completely

Answer 33

infection of the larynx, pharynx, or deep neck space

Question 34

what imaging to see retropharyngeal abscess

Answer 34

CT with contrast

Question 35

difference in the dishcarge of chlamdia and gon conjunctivitis?

Answer 35

chlamyd is more watery, mucoud discharge and less purulent than gonococcla

Question 36

how to prevent gonoccocal conjunctivitis

Answer 36

topical erythromycin within 1 hours of birth

Question 37

most common type of leukmia in kids

Answer 37

ALL

Question 38

lymphoblasts that lack peroxidase positive granules but often contain cytoplasmic aggregates of periodic acid Schiff pos material (PAS)

Answer 38

ALL

Question 39

peroxidase pos material

Answer 39

in myeloblasts

Question 40

histologic starry sky appearance

Answer 40

burkitt lymphoma (which responds well to chemo due to high mitotic rate

Question 41

auer rods

Answer 41

acute myelocytic leukemia (AML)

Question 42

myelodysplastic syndromes

Answer 42

clonal stem cell disorders which may progress to acute leukemias; usually seen in elderly patients and characterized by pancytopenia

Question 43

TdT positive staining

Answer 43

expressed only by pre B and pre T lymphoblasts

Question 44

recurrent sinopulm infections, oral candidiasis, persistent diarrhea, opportunistic infection and viral infections

Answer 44

SCID

Question 45

absent lymph nodes and tonsils, lymphopenia, absent thymic shadow on chest xray, and abnormal T, B, and natural killer cell enumeration

Answer 45

SCID

Question 46

common variable immunodeficiency is the same as

Answer 46

acquired hypogammaglobinemia

Question 47

CVID

Answer 47

manifest at later age (15 yo), serum concentrations of IgG, IgA, IgM and IgE may be decreased; NO absence or decrease in the number of B cells

Question 48

x-linked agammaglobineumia

Answer 48

aka Bruton’s agammaglobinemia

Question 49

male infant who is initially asymptomatic until 6-9 mo, when he begins to have recurrent Strep pneumo or H flu infections

Answer 49

Bruton’s agammaglobinemia