peds104

Question 1

decreased IgG, IgA, IgM, and IgE, along with absent or markedly decreased B cells

Answer 1

Brutton’s agammaglobulinemia

Question 2

onset of recurrent bacterial infections in the first 5 yr of life; serum IgG, IgM, and IgA low; absent isohemagglutinins or poor response to vaccines; less than 2percent cd19 pos B cells

Answer 2

brutton’s agammaglobulinemia

Question 3

boy with eczema, thrombocytopenia, and recurrent infections with encapsulated germs

Answer 3

wiskott-aldrich syndrome

Question 4

presents at birth with petechiae, bruises, bleeding from circumcision, or bloody stools

Answer 4

wiskott-aldrich

Question 5

low IgM, high IgA and IgE; poor antibody response to polysaccharide antigens, modertely reduced T cells and platelets

Answer 5

wisott-aldrich syndrome

Question 6

recurrent and uncontrolled infections with catalase-pos organisms

Answer 6

chronic granulomatous disease

Question 7

lymphadenitis, and abscesses of the skin and viscera (liver); lymphocytes are normal

Answer 7

chronic granulomatous disease

Question 8

an immediate anaphylactic reaction, an encephalopathy, or any CNS complication within 7 days of DTAP, means do what for the next dose?

Answer 8

only give DT; the acellular pertussis is prob responsible so we hold off on that

Question 9

by age 1 yo, what should weight and height be?

Answer 9

weight should triple and height should increase by 50 percent

Question 10

twice daily administration of prophylactic penicillin should be given to kids with sickle ceel disease until hwen

Answer 10

5 years of age

Question 11

infant with cyanosis that is aggravated by feeding nad relieved with crying

Answer 11

choanal atresia

Question 12

management of choanal atresia

Answer 12

place an oral airway and lavage feeding; definitive treatment is repairing the obstruction with surgery or endoscopy

Question 13

inspiratory stridor that is exacerbated by any exertion; symptoms appear in the first 2 weeks of life an dincrease in severity

Answer 13

laryngomalacia

Question 14

caf au lait spts, macrocephaly, feeding problems, short stature, learning disabilities

Answer 14

NF type 1

Question 15

bilateral acoustaic neuromas and cataracts

Answer 15

NF type 2

Question 16

fine reticular granulatiry of the lung parenchyma

Answer 16

classic in hyaline membrane disease

Question 17

chest xray shouws prominent pulmonary vascular markings,, fluid lines in the fissures, overaeration, a flat diaphragm, and occasionally pleural fluid

Answer 17

transient tachypnea of the newborn

Question 18

persistent pulm htn of the newborn

Answer 18

cyanosis; persistence of fetal circulatory pattern of R to L shunting; hypoxia unresponsive to 100percent oxygen;

Question 19

meconium aspiration can lead to pneumothorax or pneumodiastinum

Answer 19

right

Question 20

patchy infiltrates, coarse streaking of both lung fields, increased anterposteriod diameter, and flattening of the diaphrag,

Answer 20

chest xray in meconium aspiration

Question 21

osgood schlatters disease

Answer 21

aka traction apophysitis

Question 22

what bacteria is associated with infants with indwelling IV catheters

Answer 22

coag neg staph

Question 23

most common causes of early onset and late sepsis

Answer 23

GBS and E coli

Question 24

hypotonia, hepatosplenomegaly, cervical lymphadenopath, protruding abdomen, cherry red spon on macula, regression of milestones

Answer 24

niemann-pick disease