Flashcards in T2-GI Disorders: Hirschprung Disease Deck (17):
What is another name for Hirshprung disease?
Congenital aganglionic magacolon
Hirshprung disease is the most common cause of _____
Hirshprung disease is ___ more common in males
Is this familial?
In some cases
Is this disease associated with other diseases?
Yes, Down Syndrome
Hirshprung disease is the absence of _____ in the bowel.
Where is this most often in?
What does Hirsphrung disease result in?
Portion of the colon not having motility
Hirshprung disease causes accumulation of _____
What is proximal to the defect?
Clinical manifestation: Failure to pass meconium within ____ of birth
What are some other clinical manifestations of Hirschsprung's Disease?
-Refusal to feed
-Bile stained vomitus
-Intestinal obstruction (may have explosive stools)
What would a bowel x-ray show?
Dilated loops of bowel
What with a biopsy of the intestine show?
Absence og ganglion cells
What will an anorectal manometry show?
Failure of the internal sphincter to relax
What are the 2 stages for the surgical intervention for hirshprungs?
Stage 1: Colostomy
Stage 2: Repositioning of healthy bowel, closure of colostomy