T2-GI Disorders: Hirschprung Disease Flashcards Preview

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Flashcards in T2-GI Disorders: Hirschprung Disease Deck (17):
1

What is another name for Hirshprung disease?

Congenital aganglionic magacolon

2

Hirshprung disease is the most common cause of _____

Neonatal obstruction

3

Hirshprung disease is ___ more common in males

4x

4

Is this familial?

In some cases

5

Is this disease associated with other diseases?

Yes, Down Syndrome

6

Hirshprung disease is the absence of _____ in the bowel.

Ganglion cells

7

Where is this most often in?

Rectosigmoid region

8

What does Hirsphrung disease result in?

Portion of the colon not having motility

9

Hirshprung disease causes accumulation of _____

Intestinal contects

10

What is proximal to the defect?

Bowel distention

11

Clinical manifestation: Failure to pass meconium within ____ of birth

24-48 hours

12

What are some other clinical manifestations of Hirschsprung's Disease?

-FTT
-Poor feeding
-Refusal to feed
-Chronic constipation
-Abdominal distention
-Bile stained vomitus
-Intestinal obstruction (may have explosive stools)

13

What would a bowel x-ray show?

Dilated loops of bowel

14

What with a biopsy of the intestine show?

Absence og ganglion cells

15

What will an anorectal manometry show?

Failure of the internal sphincter to relax

16

What are the 2 stages for the surgical intervention for hirshprungs?

Stage 1: Colostomy
Stage 2: Repositioning of healthy bowel, closure of colostomy

17

Post op care for Hirschsprungs?

-NPO
-NG tube
-May have foley cath immediate post op
-IV fluids
-Ostomy care
-Discharge planning

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