Comgenital Long QT

Question 1

Congenital long qt syndrome can predispose to

Answer 1

Polymorphic ventricular tachycardia (ie Torsades de pointes), with increased risk of syncope and sudden cardiac death (especially during periods of high sympathetic activity/ increased HR)

Question 2

Long qt syndrome tx

Answer 2

Beta blockers (propranolol, nadolol)

(Dampen sympathetic activity and shorten qt interval at high heart rates reducing risk of syncope and sudden cardiac death)

Question 3

genetic and syndromes with Congenital long qt can be associated with

Answer 3

Sensiorneural hearing loss and other cardiac manifestations