PATHOMA- vasculitis Flashcards Preview

BL/DD USMLE and Basics > PATHOMA- vasculitis > Flashcards

Flashcards in PATHOMA- vasculitis Deck (20)
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1
Q

vasculitis is defined as

A

inflammation of the blood vessel wall

2
Q

general symptoms of vasculitis

A

non specific inflammation symptoms

organ ischemia

3
Q

vasculitis is split into

A

vessel size

4
Q

large vessel vasculitis type

A

temporal (giant cell) arteitis
takayas arteitis

*Aorta an its major branchs

5
Q

Medium vessel vasculitis type

A

polyarteritis nodosa
kawasaki disease

*muscular art that supply organs

6
Q

Small vessel vasculitis type

A

Wegener granulomatosis
Microscpoic Polyangitis
Chug Strous Small Cell
Henoch–Schönlein purpura

7
Q

Adults over 50
Temporal artery (HA)
Opthalmic artery (vision chnages)
Jaw Claudation

A

temporal (giant cell) arteitis

8
Q

Adults under 50
usually Asian women
Affctes proximally
neuro involvement

A

takayas arteitis

9
Q

Elevated ESR
Granulomitis Inflamation
Presence of giant cells on biopsy

A

temporal (giant cell) arteitis/takayas arteitis

10
Q
Young Adult 
Necrotizing 
Lungs are spared 
affects large organs
related to Hep B
A

Polyaritis Nodosa

11
Q

Asain children under 4
non-specific symptoms
Coronary Art
Can lead to MI Aspirin as Rx

A

kawasaki disease

12
Q

takayas arteitis

A

Adults under 50
usually Asian women
Affctes proximally
neuro involvement

13
Q

Never has lung symptoms
Nodules of fibrosis on artery tissue
FATAL without corticosteriod treatment

A

Polyaritis Nodosa

14
Q

Wegener Granulomatosis

A

Wegener Granulomatosis

15
Q

ANCA Test

A

Slide with neutrophils
add pt serum
if serum has AB, it will bind

P-ANCA- binds near nucleus
C-ANCA- binds in cytoplasm

16
Q

Looks like Wegener Granulomatosis
Affects lung and kidney
P-ANCA+

A

Microscopic Polyangitis

17
Q
IgA-IC deposition 
common in children 
has Palipable Purpura 
IgA nephropathy 
Often after a URI
A

Henoch–Schönlein purpura

18
Q

Which vasculitis is P-ANCA and related to asthma?

A

Chug Strous Small Cell

19
Q

Wegener Granulomatosis

A

Wegener Granulomatosis

20
Q

Microscopic Polyangitis

A

Looks like Wegener Granulomatosis
Affects lung and kidney
P-ANCA+