Esenmenger’s Syndrome

Question 1

What does Eisenmenger’s syndrome describe?

Answer 1

The reversal of a left-to-right shunt in a congenital heart defect due to pulmonary hypertension

This occurs when an uncorrected left-to-right leads to remodeling of the pulmonary microvasculature.

Question 2

What causes Eisenmenger’s syndrome?

Answer 2

Pulmonary hypertension resulting from an uncorrected left-to-right shunt

This leads to obstruction to pulmonary blood flow.

Question 3

What congenital heart defects are associated with Eisenmenger’s syndrome?

Answer 3

• Ventricular septal defect
• Atrial septal defect
• Patent ductus arteriosus

These defects can lead to the development of pulmonary hypertension.

Question 4

What are some features of Eisenmenger’s syndrome?

Answer 4

• Original murmur may disappear
• Cyanosis
• Clubbing
• Right ventricular failure
• Haemoptysis
• Embolism

These features indicate the severity and complications of the syndrome.

Question 5

What is required for the management of Eisenmenger’s syndrome?

Answer 5

Heart-lung transplantation

This is often necessary due to the severity of the condition.